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"lead": "Опущенное верхнее веко или птоз - (от др.-греч. πτῶσις «падение», также: птоз верхнего века, блефароплегия, блефароптоз)[3][4] — патологическое низкое положение верхнего века по отношению к глазному яблоку вследствие его опущения.\r\nРазновидности\r\n\r\nПолный врождённый правосторонний птоз\r\nОдносторонний или двухсторонний\r\nВрождённый или приобретённый\r\nПолный или частичный\r\nПричины\r\nПричиной врождённого птоза является недоразвитие или отсутствие мышцы, поднимающей верхнее веко.\r\nПричиной приобретённого птоза являются, помимо травм, многие неврологические заболевания (инсульт, энцефалит и др., часто в рамках синдрома Горнера), ведущие к парезу или параличу глазодвигательного нерва, иннервирующего мышцу, поднимающую верхнее веко.\r\nДиагностика\r\nПри оценке степени птоза пользуются параметром MRD — расстоянием между краем верхнего века и центром зрачка в мм. Так, если край века проходит через середину зрачка — это MRD = 0 мм, если край века выше середины зрачка, то MRD может быть от +1 до +5, +6, если ниже середины зрачка, то MRD будет — 1-5 мм.\r\n\r\nПри определении степени птоза и подвижности верхнего века важно фиксировать брови пациента в расслабленном положении, так как нередко удается открывать глаз с полным птозом до состояния, походящего на птоз 2-й и даже 1-й степени за счёт сильного напряжения лобной мышцы и бровей.\r\n\r\nУ детей малого возраста особенно важно определить есть ли амблиопия, так как сниженное зрение — показание к коррекции птоза. Если речь идёт о ребёнке до 2-3 лет, когда определение остроты зрения по оптотипам не представляется возможным по понятным причинам, можно заподозрить наличие сниженного зрения, оценивая реакцию ребёнка на прикрывание «хорошего» глаза, при условии, что веко на глазу с птозом принудительно открыто (например пластыревой подвеской). Так, при сниженном зрении на стороне поражения ребёнок будет негативно относиться к прикрыванию здорового глаза — отталкивать руку, плакать и т. п. Значит, глаз видит существенно хуже.\r\n\r\nДалее важно оценить силу леватора, экскурсию века, высоту и вид пальпебральной складки, напряжённость бровей, наличие лагофтальма, феномен Белла и продукцию слезной жидкости. Внимательно осматривают роговицу, чтобы выявить любые поражения или проявления дистрофии, которые могут предрасполагать к послеоперационной кератопатии у пациента. Экзофтальм или «отставание» века может создавать впечатление о наличии птоза на парном глазу. Поэтому полезно выполнить экзофтальмометрию.\r\n\r\nЛечение\r\nЛечение птоза подразделяется на консервативное и хирургическое. Консервативному лечению подлежит нейрогенный птоз. Терапия направлена на восстановление функции нерва. Применяется местная УВЧ терапия, гальванотерапия, препараты для питания нервной ткани. В отсутствие эффекта от консервативного лечения нейрогенного птоза и во всех остальных случаях прибегают к хирургическому лечению.\r\n\r\nВажным этапом в ожидании оперативного лечения у детей младшего возраста с птозами 2-й и 3-й степени является подвешивание верхнего века к коже лба с помощью лейкопластыря. Эта манипуляция имеет плохой косметический эффект и создаёт определённые неудобства, но позволяет избежать депривации и развития амблиопии, а также выиграть время для подготовки ребёнка к хирургическому лечению. Важно обучить родителя правильной технике выполнения данной манипуляции: слегка потянуть верхнее веко вниз, для расправления имеющихся складок кожи, узкую (1 см) полоску пластыря одним концом плотно приклеиваем к коже верхнего века в проекции роговицы, отступив от края века на 3—4 мм, подтягиваем полоску пластыря вверх до открытия большей площади зрачка, затем плотно приклеиваем другой конец полоски к коже лба над бровью. При этом следует придерживаться следующих правил:\r\n\r\nне нужно давить на глазное яблоко;\r\nне нужно добиваться строгой симметрии в положении век обоих глаз;\r\nнужно строго следить за тем, чтобы величина неполного смыкания век при спокойном закрытии обоих глаз не была более 2,0—2,5 мм;\r\nиспользовать пластырь-подвеску в период наибольшего времени бодрствования, не менее 3 часов в день;\r\nне использовать во время сна;\r\nпри контактном дерматите отменить пластырь-подвеску, а затем использовать лейкопластырь другой фирмы (или той же);\r\nпротирать кожу влажным тампоном от клейкого вещества после снятия пластыря.\r\nПри невозможности проведения пластыревого подвешивания (ребёнок срывает пластырь, выраженные аллергические реакции, социальная дезадаптация пациента в детском коллективе из-за издевательств по поводу приклееного пластырем века) целесообразно проведение хирургического лечения в сроки от 6 месяцев, поскольку ожидание ранее принятого в России срока проведения хирургического лечения (3—4 года и позже) гарантированно приведёт к развитию стойкой амблиопии.\r\n\r\nПодавляющее большинство случаев птоза лечится хирургическим способом.",
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"lead": "Нарушения зрения — снижение способности видеть до такой степени, что вызывает проблемы, не устраняемые обычными способами, такими как очки или лекарства.[1][2][3]\r\n\r\nЭто может быть из-за болезни, травмы, врождённых или дегенеративных заболеваний. Эта потеря зрения, как правило, определяется как:\r\n\r\nОстрота зрения с коррекцией менее 20/60, или значительный дефект центрального поля,\r\nЗначительный одноимённый или разноимённый двусторонний визуальный дефект периферического поля, включающий дефект поля или общее сжатия или сужение поля, или\r\nПониженный пик контрастной чувствительности с любым из указанных выше условий.[1][2][3][4]\r\nГлазные нарушения, которые могут привести к нарушениям зрения могут включать в себя дегенерацию сетчатки, альбинизм, катаракты, глаукомы, мышечные проблемы, которые приводят к нарушениям зрения, расстройства роговицы, диабетическую ретинопатию, врождённые пороки и инфекции. Нарушения зрения также могут быть вызваны расстройствами мозга и нервной системы, в этом случае их, как правило, называют кортикальными нарушениями зрения (CVI). Путеводитель оценки постоянного ухудшения американской медицинской ассоциации попытался представить «стандартизированный, объективный подход к оценке медицинских нарушений». Глава Визуальная система «устанавливает критерии для оценки постоянного ухудшения зрительной системы, как это влияет на способность человека выполнять действия в повседневной жизни».[5] Путеводитель оценил, что потеря одного глаза составляет 25 % нарушений зрительной системы и 24 % от полного обесценивания человека;[5][6]. Полная потеря зрения на оба глаза, как считается, является 100 % нарушением зрения и 85 % от полного обесценивания человека[5]\r\n\r\nВизуальные нарушения наносят значительный экономический удар даже в развитых странах.[7] Значительную часть глобального нарушения зрения можно предупредить.",
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"lead": "Опущенное верхнее веко или птоз - (от др.-греч. πτῶσις «падение», также: птоз верхнего века, блефароплегия, блефароптоз)[3][4] — патологическое низкое положение верхнего века по отношению к глазному яблоку вследствие его опущения.\r\nРазновидности\r\n\r\nПолный врождённый правосторонний птоз\r\nОдносторонний или двухсторонний\r\nВрождённый или приобретённый\r\nПолный или частичный\r\nПричины\r\nПричиной врождённого птоза является недоразвитие или отсутствие мышцы, поднимающей верхнее веко.\r\nПричиной приобретённого птоза являются, помимо травм, многие неврологические заболевания (инсульт, энцефалит и др., часто в рамках синдрома Горнера), ведущие к парезу или параличу глазодвигательного нерва, иннервирующего мышцу, поднимающую верхнее веко.\r\nДиагностика\r\nПри оценке степени птоза пользуются параметром MRD — расстоянием между краем верхнего века и центром зрачка в мм. Так, если край века проходит через середину зрачка — это MRD = 0 мм, если край века выше середины зрачка, то MRD может быть от +1 до +5, +6, если ниже середины зрачка, то MRD будет — 1-5 мм.\r\n\r\nПри определении степени птоза и подвижности верхнего века важно фиксировать брови пациента в расслабленном положении, так как нередко удается открывать глаз с полным птозом до состояния, походящего на птоз 2-й и даже 1-й степени за счёт сильного напряжения лобной мышцы и бровей.\r\n\r\nУ детей малого возраста особенно важно определить есть ли амблиопия, так как сниженное зрение — показание к коррекции птоза. Если речь идёт о ребёнке до 2-3 лет, когда определение остроты зрения по оптотипам не представляется возможным по понятным причинам, можно заподозрить наличие сниженного зрения, оценивая реакцию ребёнка на прикрывание «хорошего» глаза, при условии, что веко на глазу с птозом принудительно открыто (например пластыревой подвеской). Так, при сниженном зрении на стороне поражения ребёнок будет негативно относиться к прикрыванию здорового глаза — отталкивать руку, плакать и т. п. Значит, глаз видит существенно хуже.\r\n\r\nДалее важно оценить силу леватора, экскурсию века, высоту и вид пальпебральной складки, напряжённость бровей, наличие лагофтальма, феномен Белла и продукцию слезной жидкости. Внимательно осматривают роговицу, чтобы выявить любые поражения или проявления дистрофии, которые могут предрасполагать к послеоперационной кератопатии у пациента. Экзофтальм или «отставание» века может создавать впечатление о наличии птоза на парном глазу. Поэтому полезно выполнить экзофтальмометрию.\r\n\r\nЛечение\r\nЛечение птоза подразделяется на консервативное и хирургическое. Консервативному лечению подлежит нейрогенный птоз. Терапия направлена на восстановление функции нерва. Применяется местная УВЧ терапия, гальванотерапия, препараты для питания нервной ткани. В отсутствие эффекта от консервативного лечения нейрогенного птоза и во всех остальных случаях прибегают к хирургическому лечению.\r\n\r\nВажным этапом в ожидании оперативного лечения у детей младшего возраста с птозами 2-й и 3-й степени является подвешивание верхнего века к коже лба с помощью лейкопластыря. Эта манипуляция имеет плохой косметический эффект и создаёт определённые неудобства, но позволяет избежать депривации и развития амблиопии, а также выиграть время для подготовки ребёнка к хирургическому лечению. Важно обучить родителя правильной технике выполнения данной манипуляции: слегка потянуть верхнее веко вниз, для расправления имеющихся складок кожи, узкую (1 см) полоску пластыря одним концом плотно приклеиваем к коже верхнего века в проекции роговицы, отступив от края века на 3—4 мм, подтягиваем полоску пластыря вверх до открытия большей площади зрачка, затем плотно приклеиваем другой конец полоски к коже лба над бровью. При этом следует придерживаться следующих правил:\r\n\r\nне нужно давить на глазное яблоко;\r\nне нужно добиваться строгой симметрии в положении век обоих глаз;\r\nнужно строго следить за тем, чтобы величина неполного смыкания век при спокойном закрытии обоих глаз не была более 2,0—2,5 мм;\r\nиспользовать пластырь-подвеску в период наибольшего времени бодрствования, не менее 3 часов в день;\r\nне использовать во время сна;\r\nпри контактном дерматите отменить пластырь-подвеску, а затем использовать лейкопластырь другой фирмы (или той же);\r\nпротирать кожу влажным тампоном от клейкого вещества после снятия пластыря.\r\nПри невозможности проведения пластыревого подвешивания (ребёнок срывает пластырь, выраженные аллергические реакции, социальная дезадаптация пациента в детском коллективе из-за издевательств по поводу приклееного пластырем века) целесообразно проведение хирургического лечения в сроки от 6 месяцев, поскольку ожидание ранее принятого в России срока проведения хирургического лечения (3—4 года и позже) гарантированно приведёт к развитию стойкой амблиопии.\r\n\r\nПодавляющее большинство случаев птоза лечится хирургическим способом.",
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},
"code": "Q11.2",
"name": "Микрофтальм",
"icd_name": "Микрофтальм",
"gender": 0,
"age_min": 1,
"age_max": 100,
"cause": [
"0"
],
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"slug": "q11.2_mikroftalm",
"lead": "значительно уменьшенное в размерах глазное яблоко",
"description": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Микрофтальм – это уменьшение глазного яблока в размере, при котором его продольная ось не превышает 21 мм у взрослого человека и 19 мм у ребёнка.</span></p>",
"etiology": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Микрофтальм относится к семейно наследственному характеру возникновения. Установить причину истинной этиологии очень сложно, вариант взятия пуповинной крови сразу после рождения, является наиболее эффективным в выявлении возникновения заболевания на фоне каких либо инфекции, это единственный информативный анализ. Провоцировать возникновение могут:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Группа TORCH-инфекций. При поражении организма матери и плода внутриутробными инфекциями, такими как: токсоплазмоз, краснуха, и инфекции герпесного типа, но только при первичном заражении, при повторно перенесенных инфекциях в организме матери существуют анти тела, которые защищают плод от поражения. Очень маленький процент инфицирования плода при повторном заражении. Первично перенесенные инфекции вызывают очень серьезные патологии, сопровождающие микрофтальм, это волчья пасть и заячья губа, микроцефалия, нарушение развития внутренних органов.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Токсическое. Воздействие токсических веществ, малое радиационное облучение, интоксикация алкоголем, наркотиками. Не контролируемое употребление лекарственных препаратов. Повышает риск возникновения микрофтальма.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Синдром амниотических перетяжек. Образует жесткие стяжки, которые могут сдавливать органы зрения. Самая маловероятная разновидность причины возникновения патологии.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Генетические синдромы. Сопровождаются различными поражениями всех органов и систем плода, где микрофтальм, как сопутствующая патология.</span></li>\r\n</ul>\r\n<p> </p>\r\n<p><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\"> </span></p>",
"pathogenesis": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Ведущая роль в развитии микрофтальма отводится действию тератогенных факторов. Степень выраженности гипоплазии глаза коррелирует со временем воздействия патологических агентов. Чем раньше наступает тератогенное или эмбриотоксическое влияние – тем ниже уровень дифференцировки глазного яблока. Доказано, что возникновение данного порока развития ассоциировано с точечными мутациями генов. Хромосомные мутации обуславливают вторичное развитие аномалии глаза как одного из множественных проявлений генетического синдрома. Возникновение «колобоматозной» формы в большинстве случае обусловлено амниотическими сращениями.</span></p>",
"diagnostics": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Для постановки диагноза проводится наружный осмотр, специальное офтальмологическое исследование. Ввиду того, что микрофтальм часто является симптомом генетической патологии, дополнительно показан генетический ДНК-анализ, материалом для которого служит кровь или буккальный эпителий. Офтальмологическое обследование включает:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Биомикроскопию глаз. Проводится с целью выявления патологических изменений переднего отдела глаз, помутнения оптических сред, оценки состояния пальпебральной и орбитальной конъюнктивы.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Визометрию. Методика применяется для определения остроты зрения.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Рефрактометрию. Исследование позволяет изучить оптические свойства глаза и диагностировать аномалии рефракции (миопию, гиперметропию, астигматизм).</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">УЗИ глаз. Метод используют с целью осмотра глазного яблока, определения эхогенности его структур, выявления множественных кист.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">КТ орбиты. Осуществляется перед предполагаемым оперативным вмешательством для оценки анатомо-физиологических особенностей строения костных стенок, распределения периорбитальной клетчатки.</span></li>\r\n</ul>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Пациентам с микрофтальмом показана консультация генетика.</span></p>\r\n<p><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\"> </span></p>",
"treatment": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Лечебная тактика при микрофтальме определяется степенью гипоплазии глазного яблока и длительностью течения заболевания. В основе лечения лежит оперативная коррекция. Консервативная терапия применяется только с целью профилактики вторичных осложнений и базируется на инсталляциях растворов антисептиков. Хирургическое лечение включает:</span></p>\r\n<ul style=\"margin-top: 0; margin-bottom: 0; padding-inline-start: 48px;\">\r\n<li><span style=\"font-size: 7pt; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Задний бандаж склеры. Операция показана при незначительной гипоплазии глаза (уменьшение переднезадней оси не более чем на 3 мм). В ходе вмешательства под прямыми мышцами проводят полоски аллотрансплантата с последующим прикреплением к эписклере. При необходимости возможна повторная операция.</span></li>\r\n<li><span style=\"font-size: 7pt; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Косметическое глазопротезирование. Применяется при выраженной гипоплазии (5 мм и более). Использование тонкостенного протеза позволяет сохранить подвижность глазного яблока. При повышенной чувствительности роговицы показана ее деэпителизация. На поверхность роговой оболочки укладывают округлый аллотрансплантат.</span></li>\r\n<li><span style=\"font-size: 7pt; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Имплантационная методика. Этот метод используют, если переднезадний вектор не превышает 10 мм. В ходе операции кожно-жировой трансплантат помещают в ретробульбарное пространство и выполняют отсроченное протезирование.</span></li>\r\n</ul>",
"prevention": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Специфические превентивные меры отсутствуют. Неспецифическая профилактика включает предотвращение действия тератогенных факторов, своевременную диагностику и лечение TORCH-инфекций. При отягощенном наследственном анамнезе рекомендовано проведение генетического скрининга.</span></p>",
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