ВОзвращает список болезней. Можно фильтр/искать

search, age, gender, parent, symptoms, sort_name, sort_by, rand, branches
GET /disease/?format=api&ordering=name&page=71
HTTP 200 OK
Allow: GET, HEAD, OPTIONS
Content-Type: application/json
Vary: Accept

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            "code": "Q03",
            "name": "Врожденная гидроцефалия",
            "icd_name": "Врожденная гидроцефалия",
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            "age_min": 0,
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            "slug": "q03_vrozhdennaya_gidrocefaliya",
            "lead": "Нарушение здоровья, относящееся к группе врожденные аномалии [пороки развития] нервной системы",
            "description": " \r\nВрожденная гидроцефалия – это патологическое состояние, которое сопровождается накоплением спинномозговой жидкости в желудочках мозга из-за ее избыточной продукции, нарушения всасывания или препятствие на пути оттока. ",
            "etiology": "<p>К причинам врожденной гидроцефалии относятся пороки развития ликворной системы : </p>\r\n<ul>\r\n<li>атрезия отверстий, соединяющих желудочки мозга (Мажанди и Люшка); </li>\r\n<li>дефекты в строении подпаутинного пространства; </li>\r\n<li>сужение (стеноз) сильвиевого водопровода;  </li>\r\n<li>краниовертебральные аномалии (аномалии границы между основанием черепа и верхнешейным отделом позвоночника) - аномалия Киари, врожденная базилярная импрессия. </li>\r\n</ul>\r\n<p>Причинами врожденной гидроцефалии могут также быть внутриутробные инфекции (токсоплазмоз, врожденный сифилис, цитомегалия, краснуха), родовая травма. </p>",
            "pathogenesis": "<p>Традиционно модель гидроцефалии трактуется как дисбаланс между продуцированием и абсорбцией черепно-мозговой жидкости. Современные исследования показывают, что основная роль определяется абсорбцией капиллярами мозга. Гемодинамический патогенез гидроцефалии (первичная и вторичная) определяется нарушением венозного оттока (обструктивная гидроцефалия) и уменьшением артериальной пульсации (сообщающаяся гидроцефалия).</p>",
            "diagnostics": "<p>Гидроцефалия может быть выявлена у плода в перриод внутриутробного развития при проведении скрининга беременной женщины. УЗИ плода позволяет обнаружить гидроцефалию у ребенка на 16–20 неделе беременности. После рождения у некоторых детей гидроцефалия выявляется сразу в родильном доме специалистом-неонатологом. </p>\r\n<p>Трансиллюминация (диафаноскопия) черепа позволяет выявить наружную гидроцефалию у детей, исключить гидроанэнцефалию и субдуральную гигрому.  Суть его в просве­чивании головы пучком света от лампы в затемнённом помещении. В их лучах при гидро­цефалии начинает светиться вся голова. </p>\r\n<p>Рентгенография черепа – выявляют истончение костной ткани, расхождение швов черепа, на внутренней поверхности черепной коробки присутствует характерный симптом “пальцевидных вдавлений”. </p>\r\n<p>Магнитно-резонансная и компьютерная томография позволяют с большой точностью визуализировать патологические изменения внутри черепа, выявить место, которое препятствует оттоку ликвора. </p>\r\n<p>Ультрасонография – ультразвуковое исследование головного мозга через открытый большой родничок. Позволяет определить степень повышения внутричерепного давления. </p>\r\n<p>Офтальмоскопия – осмотр глазного дна. Выявляют застойные диски зрительных нервов, как следствие повышенного внутричерепного давления. </p>\r\n<p>Для оценки давления цереброспинальной жидкости, исследования ее состава и проведения ликвородинамических проб прибегают к вентрикулярной и люмбальной пункциям.  </p>",
            "treatment": "<p>Основными принципами лечения гидроцефалии у детей является снижение продукции спиномозговой жидкости и нормализация ее циркуляции по ликвороносным путям, в т. ч. с помощью создания обходных анастомозов. </p>\r\n<p>С целью снижения продукции ликвора и внутричерепного давления проводится дегидратационная терапия диуретиками, ингибиторами карбоангидразы, салуретиками. При прогрессирующем нарастании гидроцефалии у детей в течение 2—3-х месяцев ставится вопрос о хирургическом вмешательстве. </p>\r\n<p>Оптимальный способ оперативного вмешательства определяется этиологией, формой, стадией гидроцефалии у детей. В настоящее время все виды операций при гидроцефалии у детей могут быть поделены на 5 групп: </p>\r\n<ul>\r\n<li>паллиативные вмешательства, позволяющие временно снизить внутричерепное давление и устранить краниоцеребральную диспропорцию (люмбальные и вентрикулярные пункции, наружное вентрикулярное дренирование) </li>\r\n<li>операции, направленные на подавление ликворопродукции (клипирование, коагуляция сосудистого сплетения) </li>\r\n<li>операции, направленные на восстановление естественных путей циркуляции ликвора или создание новых путей ликворооттока (удаление опухолей, внутричерепных гематом , вентрикулостомия) </li>\r\n<li>операции, активизирующие ликворосорбцию (рассечение арахноидальных спаек и др.) </li>\r\n<li>шунтирующие операции, предусматривающие отведение ликвора в другие системы организма (вентрикулоперитонеальное шунтирование, люмбоперитонеальное шунтирование, вентрикулоатриарное шунтирование, вентрикулоцистерностомия, кистовентрикулоперитонеостомия, субдуроперитонеостомия). При невозможности выполнения стандартных шунтриующих операций проводятся атипичные шунтирующие вмешательства - вентрикулоплевральное, вентрикулоуретральное вентрикулобиллиарное шунтирование. Ликворошунтирующие операции при гидроцефалии у детей сопряжены с риском нарушения функционирования дренажных систем, гипердренированием или осложнениями воспалительного характера.  </li>\r\n</ul>",
            "prevention": "<p>Чтобы предупредить развитие врожденной гидроцефалии  необходимо: </p>\r\n<ul>\r\n<li>Защищаться от инфекционных заболеваний во время беременности </li>\r\n<li>Не принимать никаких медикаментов во время беременности, кроме тех, которые прописал врач </li>\r\n<li>Профилактическое плановое УЗИ-обследование беременных женщин и нейроультрасонография у младенцев. </li>\r\n</ul>",
            "clinical_picture": "<p>У детей из-за большой податливости костей черепа не наблюдается повышения внутричерепного давления, гидроцефалия у них сопровождается увеличением размеров черепа. У новорожденных и детей раннего возраста гидроцефалия характеризуется слишком большим размером головы, выбуханием вен скальпа, напряжением и отсутствием пульсации большого родничка, отеком дисков зрительных нервов. Часто отмечается симптом «заходящего солнца» - ограничение движений глазных яблок кверху. Может наблюдаться расхождение швов черепа. Постукивание по черепу сопровождается характерным звуком (симптом «треснутого горшка»). У детей первого года жизни гидроцефалия приводит к отставанию в физическом и умственном развитии. Они позже начинают держать голову, переворачиваться, сидеть и ходить. </p>\r\n<p>Дети, у которых имеется выраженная гидроцефалия, отличаются шарообразной формой головы, ее слишком большим размером, глубоко посаженными глазами, оттопыренными ушами, истончением кожи головы. Может отмечаться снижение зрения, повышение мышечного тонуса в нижних конечностях, нарушения со стороны черепных нервов. Дети, страдающие гидроцефалией, малоподвижны, не могут следить глазами за родителями. Они раздражены, часто плачут, постоянно сонливы, плохо едят. Их часто тошнит. </p>",
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            },
            "code": "Q15.0",
            "name": "Врожденная глаукома",
            "icd_name": "Врожденная глаукома",
            "gender": 0,
            "age_min": 0,
            "age_max": 100,
            "cause": [
                "0"
            ],
            "periodicity": 1,
            "slug": "q15.0_vrozhdennaya_glaukoma",
            "lead": "наследственное заболевание, сопровождающееся постепенным увеличением внутриглазного давления и обусловленными этим сопутствующими зрительными нарушениями",
            "description": "",
            "etiology": "<p><span id=\"docs-internal-guid-badaf9d9-7fff-9248-f3ae-96bf3e1613dd\"><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">В основе заболевания лежат врожденные аномалии развития угла передней камеры и дренажной системы глаза, создающие препятствие оттоку внутриглазной жидкости или в значительной степени затрудняющие его, что приводит к повышению внутриглазного давления. Причины этой аномалии &mdash; различные патологические состояния женщины, особенно в первые месяцы беременности. Обусловливаются они самыми разнообразными причинами: инфекциями (коревая краснуха, грипп и т. д.), отравлениями, алкоголизмом, ионизирующей радиацией и пр.</span></span></p>",
            "pathogenesis": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Передняя камера глаза заполнена прозрачной жидкостью, которая омывает глазные структуры и сохраняет его оптические свойства: водянистая влага, которая для поддержания стабильного внутриглазного давления постоянно поступает и выводится из этой части глаза.</span></p>\r\n<p>&nbsp;</p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Врожденная глаукома выражается в дефекте, связанном с формой угла, образуемого при соединении роговицы с радужной оболочкой, и через который происходит дренаж водянистой влаги. Этот дефект приводит к повышению внутриглазного давления и последующему повреждению зрительного нерва.</span></p>",
            "diagnostics": "<p>&nbsp;</p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Выявление врожденной глаукомы производится врачом-офтальмологом на основании данных осмотра, офтальмологических исследований (тонометрии, гониоскопии, кератометрии, биомикроскопии, офтальмоскопии, УЗ-биометрии). Также немаловажную роль в диагностике этого состояния играют генетические исследования, изучение наследственного анамнеза и течения беременности. </span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\">&nbsp;</p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">При осмотре обнаруживаются увеличенные (при ранней форме) или нормальные размеры глаз, может также наблюдаться отек окружающих глазное яблоко тканей. Горизонтальный диаметр роговицы увеличен, на ней возможны микроразрывы и помутнение, склера истончена и имеет голубоватый оттенок, поражается при врожденной глаукоме и радужная оболочка &ndash; в ней возникают атрофические процессы, зрачок вяло реагирует на световые раздражители. Передняя камера глаза углублена (в 1,5-2 раза больше возрастной нормы).</span></p>",
            "treatment": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">При врожденной глаукоме чаще всего проводится оперативное вмешательство, при этом выбор метода операции остается за хирургом. Это зависит от стадии, вовлеченности глазных структур. Только хирургическими методами возможно создать условия для нормального оттока внутриглазной жидкости.</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Дренирование угла передней камеры. Это уникальная техника, которая позволяет в большинстве случаев привести к стабилизации глаукоматозного процесса и нормализации внутриглазного давления.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Трабекулотомия. Применяют при сильном помутнении роговицы &mdash; через разрез склеры рассекается трабекула &ndash; участок угла передней камеры для улучшения оттока внутриглазной жидкости.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Трабекулэктомия. Через разрез в склере удаляется часть трабекулы, что создает путь оттока жидкости под конъюнктиву, из-за этого идет снижение внутриглазного давления</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Гониотомия. Проводят на ранних стадиях глаукомы. Рассекается участок угла передней камеры через роговицу, эффективность операции в этом случае составляет 85%.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Комбинированная методика (трабекулотомия + трабекулэктомия)</span></li>\r\n</ul>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\">&nbsp;</p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\">&nbsp;</p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\">&nbsp;</p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\">&nbsp;</p>\r\n<p>&nbsp;</p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Все оперативные вмешательства у детей требуют применения наркоза.</span></p>",
            "prevention": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Избежать развития наследственной глаукомы практически нельзя. Но предотвратить порок, который возникает по негативным факторам, несложно. Будущей маме нужно забыть о вредных привычках, сбалансировать пищу, избегать травмы живота.</span></p>",
            "clinical_picture": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Врожденная глаукома характеризуется своеобразными клиническими проявлениями, обусловленными возрастными особенностями глаз у детей.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Если ребенка глаукома, симптомы могут быть следующими:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">повышение внутриглазного давления;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">светобоязнь, слезотечение;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">увеличение размера глазного яблока (ребенок рождается с большими, &laquo;выразительными глазами&raquo;), причем увеличение быстро прогрессирует;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">увеличение диаметра роговицы (на поздних стадиях диаметр роговицы может достигать 20 мм и более), ширины лимба;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">отек роговицы (она выглядит мутной);</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">замедление зрачковых реакций;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">изменения диска зрительного нерва.</span></li>\r\n</ul>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Врожденная глаукома нередко сочетается с одновременным развитием дефектов в других системах и органах (микроцефалия, пороки сердца, глухота, факоматозы и т. д.), так и в глазу (микрокорнеа, аниридия, катаракта и пр.).</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\">&nbsp;</p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Врожденная глаукома в 75% наблюдений развивается в обоих глазах. По наблюдениям специалистов, врожденная и детская глаукома у большинства детей не сопровождаются жалобами, исключая те, которые вызваны роговичным синдромом. </span></p>",
            "image": null,
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