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"lead": "состояние, характеризующееся скоплением менструальной крови во влагалище из-за закрытия его просвета",
"description": "<p><span id=\"docs-internal-guid-06c46de8-7fff-5871-dc27-31aa38f17bb2\"><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Гематокольпос — это патологическое состояние, которое характеризуется наличием неперфорированной девственной плевы (без отверстий), в результате чего во влагалище (и в полости матки) скапливается менструальная кровь</span></span></p>",
"etiology": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Причиной формирования гематокольпоса является полная непроходимость влагалища на любом уровне. Источником проблемы могут быть аномалии, развившиеся внутриутробно с пятой по двадцатую неделю беременности, или повреждения вагины, возникшие как в детском, так и во взрослом возрасте.</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Врождённые аномалии. Анатомические пороки женских гениталий, приводящие к гематокольпосу, включают атрезию гимена (полное заращение девственной плевы), поперечные и продольные вагинальные перегородки, частичную аплазию влагалища при нормально функционирующей матке. Причиной аномалий развития является воздействие тератогенных факторов. Внешние факторы включают инфекции (особенно вирусные), лекарственные препараты (прежде всего - гормональные), химические тератогены (бензин, спирты, фенолы, формальдегид), гипо- или гипервитаминоз, ионизирующее излучение. К внутренним относятся эндокринно-обменные патологии и наследственные мутации.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Приобретённые пороки. В допубертатном периоде ввиду возрастных особенностей (узости просвета влагалищной трубки, физиологической гипоэстрогении, незрелости иммунной системы) к атрезии влагалища и гимена чаще всего приводят воспаления - вульвовагиниты, обусловленные недостаточной гигиеной наружных гениталий, а также вызванные аллергической реакцией, инфекциями (герпесвирусной, хламидийной, уреа- и микоплазменной, корью, краснухой). У взрослых женщин приобретённая атрезия в большинстве случаев связана с родовыми травмами и оперативными вмешательствами.</span></li>\r\n</ul>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>",
"pathogenesis": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Приобретённые аномалии вагины обусловлены слипанием её стенок в результате воспаления или грубыми рубцовыми деформациями вследствие травм и хирургических операций. К врождённым порокам приводят нарушения развития мюллеровой системы и её слияния с урогенитальным синусом. У эмбриона женского пола маточные трубы, матка и влагалище формируются из парамезонефрических (мюллеровых) протоков, изначально имеющих вид двух сплошных тяжей. В дальнейшем эти протоки сливаются, при этом в средней и нижней части образуется канал, закрытый снизу влагалищной пластинкой и образующий однополостную матку и верхнюю часть однорукавного влагалища. Вагинальная трубка формируется в процессе слияния мюллеровой системы, влагалищной пластины и урогенительного синуса.</span></p>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Недоразвитие нижней части мюллеровых протоков влечёт аплазию вагины. При полном неслиянии мюллеровых протоков формируются две обособленные матки и два отдельных влагалища, причём одна из трубок зачастую «слепая», не сообщающаяся с внешней средой. Результатом частичного неслияния становятся продольные влагалищные перегородки. Нарушения слияния влагалищной пластинки с мюллеровой системой и с мочеполовым синусом приводят к формированию поперечных вагинальных перегородок и атрезии гимена.</span></p>",
"diagnostics": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Диагностическая программа включает:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Гинекологический осмотр. Гематокольпос можно предположить по данным анамнеза, результатам осмотра на кресле - пальпации и визуальной оценки. Так, при заращении гимена наблюдается выпячивание синюшного опухолевого образования из половой щели или выбухание всей промежности, аплазию же легко установить по небольшому чашевидному углублению на месте влагалища. Независимо от происхождения, гематокольпос характеризуется тугоэластическим подвижным образованием, расположенным в области малого таза, иногда распространяющимся в брюшную полость.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Инструментальное исследование. Зондирование влагалища позволяет выявить атрезию и определить её уровень. С помощью пункции влагалища можно получить кровянистое содержимое, свидетельствующее о гематокольпосе. По результатам МРТ и УЗИ забрюшинного пространства и малого таза можно обнаружить добавочные матку и влагалище, анатомические пороки вагины, опухоли, исходящие из половых органов и почек.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Бактериологическое исследование. С помощью бактериоскопического и культурального метода выявляют возбудителей присоединившейся инфекции и подбирают эффективный препарат для её лечения.</span></li>\r\n</ul>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>",
"treatment": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Лечение направлено не только на устранение помех, препятствующих оттоку менструальной крови, но и на восстановление репродуктивной функции. Объём хирургического вмешательства зависит от патологии, приведшей к гематокольпосу: в одних случаях это «поточная», рутинная операция, в других – сложная, требующая высокой квалификации оперирующего гинеколога. Все операции включают обязательный этап – опорожнение и санацию гематокольпоса.</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Рассечение плевы. Гименотомия выполняется при гематокольпосе, связанном с атрезией гимена. Девственная плева рассекается крестообразным разрезом, после чего на края накладывают швы во избежание повторного сращения.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Иссечение перегородки влагалища. Показано при наличии тонких поперечных мембран. Операция заключается в их рассечении с последующим бужированием вагины.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Иссечение стенки «слепого» влагалища. Назначается при удвоении вагины - наличии продольной перегородки, образующей замкнутую полость, или при добавочной матке с аплазированной вагиной. Выполняется максимальная резекция смежной стенки и формирование сообщения замкнутого влагалища с нормально функционирующим.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Пластика влагалища. Вагинопластика показана при частичной аплазии, грубых рубцовых изменениях, значительной толщине поперечной перегородки. Отсутствующие или повреждённые стенки влагалища формируются из лоскутов промежности.</span></li>\r\n</ul>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>",
"prevention": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Первичная профилактика патологии заключается в предупреждении и своевременном лечении инфекций у девочек и женщин, борьбе с травмами в родах, здоровом образе жизни, полноценном питании и исключении факторов, вызывающих тератогенное воздействие в первой половине гестации. Вторичная профилактика включает УЗИ плода в последнем триместре беременности (некоторые аномалии, влекущие впоследствии гематокольпос, можно обнаружить уже в этом периоде), профилактические осмотры детским гинекологом девочек младшего возраста и в пубертатном периоде.</span></p>",
"clinical_picture": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Клинические проявления при врождённых и приобретённых в детстве пороках влагалища развиваются в подростковом возрасте с началом месячных. У взрослых гематокольпос формируется по прошествии нескольких месяцев после травматического воздействия. Чем меньше объём «слепого» участка влагалищной трубки, тем раньше наступает и интенсивнее проявляется болевой синдром. Опорожнение гематокольпоса приводит к моментальному улучшению состояния.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">У девочек с заращением гимена ведущим симптомом является ложная аменорея, зуд и болевой синдром присоединяется позднее, через несколько месяцев, когда гематокольпос достигает определённого размера. Ноющие боли внизу живота сначала появляются в период менструации, в дальнейшем становятся постоянными и более интенсивными. Рост образования сопровождается нарушением мочеиспускания (сначала учащением, затем задержкой) и запорами. При этой форме анатомической аномалии влагалище может достигать значительных размеров и прощупываться самой пациенткой в виде внутренней «опухоли», выходящей за пределы малого таза и выбухающей в половую щель.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">В случае атрезии и аплазии влагалища также наблюдается ложная аменорея, сопровождающаяся выраженной болью и зудом уже в первые месяцы от начала менструальной функции, болевой синдром быстрее приобретает постоянный характер. Мочеиспускание и дефекация при этих формах, как правило, не нарушаются, однако скопление крови в расположенных выше полых органах начинается значительно раньше. При наличии добавочной матки со слепым «влагалищем» симптомы аналогичны признакам при атрезии девственной плевы с тем отличием, что наблюдаются скудные месячные, причём периодические боли, сопровождающие развитие гематокольпоса в добавочной вагине, могут не соответствовать менструальному циклу полностью функционирующего полового аппарата. На поздних этапах могут присоединиться кровянисто-гнойные выделения вследствие перфорации слепого влагалища в области смежной стенки.</span></p>\r\n<p><span id=\"docs-internal-guid-f5188ab0-7fff-467f-e384-938dff109c1a\"> </span></p>",
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},
"code": "N90.3",
"name": "Дисплазия вульвы неуточненная",
"icd_name": "Дисплазия вульвы неуточненная",
"gender": 2,
"age_min": 40,
"age_max": 100,
"cause": [
"0"
],
"periodicity": 1,
"slug": "n90.3_displaziya_vulvy_neutochnennaya",
"lead": "болезнь наружных половых органов женщины, проявляющаяся аномальными изменениями в строении эпителия гениталий",
"description": "",
"etiology": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Хроническая прогрессирующая инфекция ВПЧ является одной из основных причин развития дисплазии вульвы. Помимо вируса папилломы человека дисплазия может быть обусловлена следующими факторами:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">ЗППП</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">воспалительные болезни влагалища и наружных половых органов, носящие хронический характер</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">низкий иммунный статус</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">сбои в обмене веществ</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">дисфункция эндокринной системы</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">раннее вступление в половую жизнь</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">табакокурение</span></li>\r\n</ul>\r\n<p> </p>",
"pathogenesis": "",
"diagnostics": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Чтобы диагностировать появление дисплазии вульвы у пациентки и определить ее онкогенность, врачу акушеру-гинекологу нужно провести целый ряд медицинских мероприятий:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Осмотр на кресле. Первое, что сделает доктор — проведет осмотр наружных и внутренних органов пациентки. Множественные очаги поражения, язвочки, белые бляшки насторожат врача.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Кольпоскопия. Позволит провести более детальный осмотр под многократным увеличением.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Шиллер-тест. Этот метод укажет врачу, есть ли изменения эпителия в половых органах женщины. Если ткани женщины равномерно окрашиваются йодом – они здоровы. Если же врач замечает неравномерность окраса, это позволяет заподозрить развитие неблагоприятных процессов в организме пациентки.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Анализы. Первый, и самый главный в этом случае анализ, который назначит доктор – анализ на вирус папилломы человека. Этот анализ позволит не только установить, есть ли в организме пациентки ВПЧ, но и также определить его тип, если этот вирус имеется. Этот анализ играет важную роль в скрининге дисплазии вульвы, потому что именно вирус папилломы человека, по многочисленным данным, провоцирует развитие дисплазии вульвы.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Онкоцитология (цитологическое исследование). Этот анализ позволит ответить на вопрос – есть ли атипичные клетки в половых органах женщины, развивается ли у нее онкопроцесс.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Биопсия. Биопсия позволит отправить атипичные клетки на анализ и подтвердить или опровергнуть подозрение на злокачественные образования.</span></li>\r\n</ul>\r\n<p> </p>",
"treatment": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Терапия атипической гиперплазии вульвы основана на следующих подходах:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Консервативная терапия. Базируется на использовании гормональных средств, общеукрепляющих, седативных и других препаратов, а также следовании предписанному рациону. Целью консервативной терапии является уменьшение локальных проявлений заболевания, ремиссия и улучшение психологического статуса. При в положительном тесте на ВПЧ необходим прием иммуностимулирующих и противовирусных препаратов.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Хирургическая операция. Требуется в случае тяжелых форм заболевания, выраженной онкоугрозе, рецидивировании болезни и обширном поражении эпителия. Проводится поверхностная вульвэктомия, направленная на удаление наружного эпидермиса с последующей пластической реконструкцией гениталий.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Методы, альтернативные хирургической операции. Для замены оперативного вмешательства может применяться воздействие с помощью лазера, жидкого азота и радиоволн. Однако эти методики эффективны лишь на ранних стадиях болезни и нацелены на пациенток, не достигших климактерического возраста.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Фотодинамическая терапия. Метод основан на воздействии особого светового излучения на патологические клетки, которое приводит их гибели.</span></li>\r\n</ul>\r\n<p> </p>",
"prevention": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Специфические меры профилактики не разработаны. Женщинам необходимо правильно питаться, избегать беспорядочных половых связей, отказаться от пагубных привычек, применять барьерную контрацепцию во время полового акта, санировать очаги хронических инфекций и регулярно посещать врача-гинеколога.</span></p>",
"clinical_picture": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Часто атипическая гиперплазия вульвы протекает скрытно, что создает большие сложности с ее своевременным выявлением. Обнаружение заболевания почти всегда происходит при плановом осмотре или в ходе обращения к гинекологу по какой-либо проблеме. Однако иногда незначительные проявления </span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">дисплазии может заметить и не специалист. К таковым относится появление кондилом на анусе и наружных половых органах.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">При прогрессировании атипической гиперплазии вульвы в районе гениталий возникает непрекращающийся зуд, распространяющийся на влагалище и анус. К сожалению, эти проявления не являются специфическими для данного заболевания и могут отмечаться при других гинекологических патологиях. Например, они присутствуют при кольпите и вагините.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">К другим симптомам дисплазии вульвы относятся:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">отечность гениталий</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">гнойные и слизистые выделения из влагалища</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">белые бляшки на гениталиях</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">язвочки и сухость слизистых оболочек наружных половых органов</span></li>\r\n</ul>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">При переходе заболевания на более поздние стадии степень и масштаб поражения слизистых гениталий возрастают. Из-за смазанности клинической картины диагностика атипической гиперплазии на начальных этапах представляется затруднительной, что повышает риски, сопряженные с этим заболеванием.</span></p>",
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"name": "Лейкоплакия вульвы",
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"lead": "процесс, при котором кожа и слизистая половых органов покрываются патологическими новообразованиями (ороговение)",
"description": "<p><span id=\"docs-internal-guid-b706169b-7fff-de9c-c46e-4f89baabbd5c\"><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Лейкоплакия вульвы — это хронический, невоспалительный процесс с признаками дистрофии, поражающий слизистую оболочку наружных половых органов, который выражается стремительным ороговением и пролиферацией многослойного плоского эпителия.</span></span></p>",
"etiology": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Точные причины возникновения болезни современной медицине не известны, но есть ряд факторов, при которых в составе эпителия вульвы начинают происходить изменения:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">воспалительные заболевания половых органов;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">несоблюдение правил личной гигиены;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">диабет и сбои гормонального фона;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">повреждения половых органов, эрозия шейки и др.</span></li>\r\n</ul>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Провоцирующим фактором может выступить даже негативное воздействие загрязненной окружающей атмосферы.</span></p>",
"pathogenesis": "",
"diagnostics": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Для диагностирования заболевания применяют кольпоскопию и визуальный осмотр. Обязательной процедурой является проба Шиллера. Для этого проводят равномерное окрашивание слизистой раствором Люголя. Участки, которые не окрасились, хорошо видны и невооруженным взглядом. Их наличие говорит о присутствии воспалительного процесса. В неопределенных случаях проводится биопсия для дальнейшего гистологического исследования.</span></p>",
"treatment": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Лечение лейкоплакии вульвы - комплексное и длительное, учитывающее возраст и сопутствующие заболевания пациентки; включает медикаментозную терапию, диету, физиолечение, помощь психотерапевта, при необходимости - оперативное вмешательство. Рекомендуется лечебная физкультура; прогулки на свежем воздухе, молочно – растительная диета; проведение гигиенических процедур с использованием кипяченой воды и настоев трав, отказ от мыла, перманганата калия, спринцевания; устранение раздражающих факторов (шерстяного и синтетического белья, тампонов и синтетических прокладок). При лейкоплакии вульвы противопоказаны горячие ванны и длительная инсоляция.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Назначается местное противовоспалительное и противозудное лечение с использованием мазей, кремов, вагинальных шариков с гормонами, антисептиками. В гормональной терапии применяют преднизолон, эстрогены в сочетании с андрогенами, эстроген - гестагенные препараты, неконъюгированные эстрогены и производные эстриола (циклически или в режиме контрацепции 2-3 месячными курсами). Возможен прием витаминов и микроэлементов, антигистаминных препаратов, при упорном зуде – проведение новокаиновых блокад.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Современные физиопроцедуры (ультрафонофорез лекарственных средств, оксигенотерапия с модуляцией ритмов головного мозга) при лейкоплакии вульвы оказывают противовоспалительное, десенсибилизирующее действие, нормализуют обменные процессы, гормональный и психоэмоциональный фон, укрепляют иммунную систему. Коррекция психоэмоционального состояния с применением седативных средств и методик является важным элементом лечения лейкоплакии вульвы.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">При отсутствии эффекта от консервативного лечения лейкоплакии вульвы современная гинекология применяет хирургическое иссечение единичных очагов лейкокератоза скальпелем, радионожом, а также удаление их с помощью лазера и криодеструкции. В выраженных случаях лейкоплакии вульвы </span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">выполняют радикальную операцию - экстирпацию вульвы, которая при наличии признаков малигнизации комбинируется с курсами радиотерапии.</span></p>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Пациенток с лейкоплакией вульвы берут под динамическое диспансерное наблюдение гинеколога или онколога (при наличии злокачественности поражения) с обязательным кольпоскопическим и цитологическим контролем и повторными курсами лечения.</span></p>",
"prevention": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Профилактика лейкоплакии вульвы заключается в предупреждении и своевременной коррекции гормональных сбоев в организме женщины, лечении сопутствующих воспалительных и метаболических нарушений.</span></p>",
"clinical_picture": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Опасность лейкоплакии вульвы в том, что на начальной стадии распознать недуг очень сложно. Но со временем при развитии болезни возникают следующие симптомы:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">покалывания, онемение и зуд в области половых органов;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">появление отеков;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">боли и чувство дискомфорта при половом акте;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">появление эрозий, микротрещин и язв.</span></li>\r\n</ul>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">У каждого пациента патологический процесс протекает по-разному, симптомы могут наблюдаться как комплексно, так и поодиночке.</span></p>",
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}
]
}