ВОзвращает список болезней. Можно фильтр/искать

search, age, gender, parent, symptoms, sort_name, sort_by, rand, branches
GET /disease/?format=api&ordering=-image_alt&page=32
HTTP 200 OK
Allow: GET, HEAD, OPTIONS
Content-Type: application/json
Vary: Accept

{
    "count": 11794,
    "next": "http://api.symptomd.ru/disease/?format=api&ordering=-image_alt&page=33",
    "previous": "http://api.symptomd.ru/disease/?format=api&ordering=-image_alt&page=31",
    "results": [
        {
            "id": 6630,
            "symptoms": [
                {
                    "id": 2944,
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                        {
                            "name": "шумы"
                        },
                        {
                            "name": "шумное дыхание"
                        },
                        {
                            "name": "Стерторозное дыхание"
                        },
                        {
                            "name": "храпящее дыхание"
                        }
                    ],
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                    ],
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                    "name": "Хрипы ",
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                    "age_min": 1,
                    "age_max": 100,
                    "slug": "hripy",
                    "lead": "Дыхательные шумы, обусловленные сужением дыхательных путей или наличием в них патологического содержимого",
                    "image": null,
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                },
                {
                    "id": 2851,
                    "synonyms": [
                        {
                            "name": "упадок сил"
                        },
                        {
                            "name": "мышечная слабость"
                        },
                        {
                            "name": "бессилие"
                        },
                        {
                            "name": "Адинамия"
                        }
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                    ],
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                    "slug": "upadok_sil",
                    "lead": "резкий упадок сил, мышечная слабость, сопровождающаяся значительным уменьшением или полным прекращением активности",
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                {
                    "id": 2717,
                    "synonyms": [
                        {
                            "name": "Замедленная реакция"
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                    ],
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                    "slug": "zatormozhennost",
                    "lead": "Снижение скорости реакции , замедленное течение мыслительных процессов и возникновение растянутой речи с большими паузами.",
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                {
                    "id": 2950,
                    "synonyms": [
                        {
                            "name": "локальная гипертермия "
                        },
                        {
                            "name": "горячая на ощупь"
                        },
                        {
                            "name": "отек на коже"
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                        {
                            "name": "припухлость"
                        },
                        {
                            "name": "уплотнение"
                        },
                        {
                            "name": "Локализованный отек"
                        }
                    ],
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                    "lead": "Отек в конкретном месте - это повод проконсультироваться у врача",
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                {
                    "id": 3218,
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                            "name": "Частое дыхание"
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                        {
                            "name": "Тахипноэ"
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                        {
                            "name": "Неравномерное дыхание"
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                        {
                            "name": "Одышка"
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                            "name": "Часто дышу"
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            },
            "code": "J81",
            "name": "Легочный отек",
            "icd_name": "Легочный отек",
            "gender": 0,
            "age_min": 1,
            "age_max": 100,
            "cause": [
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            "periodicity": 1,
            "slug": "j81_legochnyy_otek",
            "lead": "патологическое состояние, при котором жидкость начинает скапливаться в альвеолах",
            "description": "<p><span id=\"docs-internal-guid-c8f98be1-7fff-93ba-2f4c-a817793f1295\"><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Отек легких определяется как жизнеугрожающее состояние, для которого характерен процесс накопления внесосудистой жидкости в легких. </span></span></p>",
            "etiology": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">К основным причинам развития кардиогенного отека легких относятся:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">инфаркт миокарда с подъемом сегмента ST электрокардиограммы;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">гипертонический криз;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">пароксизм мерцательной аритмии (эпизод, длящийся от 30 секунд до семи дней, проходит самостоятельно или при помощи лечения).</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">недостаточность митрального клапана (отрыв хорды сосочковой мышцы).</span></li>\r\n</ul>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\">&nbsp;</p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Основные факторы риска кардиогенного отека легких:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">постинфарктный и атеросклеротический кардиосклероз с систолической сердечной недостаточностью;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">диастолическая дисфункция миокарда у пожилых больных;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">систолическая и диастолическая дисфункция миокарда у больных с кардимиопатией или миокардитом;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">постоянная форма мерцательной аритмии;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">врожденные и приобретенные пороки левых отделов сердца;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">поражения клапанного аппарата, особенно митрального клапана, вследствие ревмокардита, инфекционного эндокардита, атеросклероза.</span></li>\r\n</ul>\r\n<p>&nbsp;</p>\r\n<p><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">&nbsp;</span></p>",
            "pathogenesis": "<p>&nbsp;</p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Альвеолы &mdash; это структурные элементы легких, в которых происходит газообмен. Обычно они заполнены воздухом. Когда в альвеолах накапливается жидкость, нарушаются процессы нормального газообмена. По различным причинам сердце не перекачивает кровь из легких. В результате кровь накапливается в кровеносных сосудах легких, а затем просачивается в просвет альвеол. Появляются признаки отека легких.</span></p>",
            "diagnostics": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Врач диагностирует состояние на основании анамнеза и типичных изменений, наблюдаемых во время обследования. При осмотре пациента с отеком легких врач слышит типичные аускультативные изменения. Показатели тонометра определяют высокое или слишком низкое АД. При пальпации определяется отек нижних конечностей (у людей с обострением хронической сердечной недостаточности).</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\">&nbsp;</p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Инструментальная диагностика отека легких:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">рентген органов грудной клетки;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">ЭКГ;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">эхокардиография сердца;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">лабораторные анализы крови;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">анализ крови на кислород и углекислый газ.</span></li>\r\n</ul>\r\n<p>&nbsp;</p>",
            "treatment": "<p>&nbsp;</p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">На первом месте при лечении отека легких стоит неотложная медицинская помощь. Требуется немедленное выполнение интенсивного лечения. Пациенту назначают кислород с высокой скоростью потока и внутривенно вводят диуретики. </span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">В зависимости от значений АД назначают соответствующие препараты для его стабилизации. Иногда, несмотря на прием лекарств, состояние пациента не улучшается и из-за недостаточной оксигенации крови. В этом случае при лечении отека легких необходимы интубация (размещение пластиковой трубки в трахее пациента для обеспечения проходимости дыхательных путей) и временная поддержка дыхания с помощью аппарата ИВЛ.</span></p>",
            "prevention": "<p>&nbsp;</p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Основная профилактика отека легких заключается в недопущении данного состояния путем лечения провоцирующего заболевания. Необходимы регулярный прием прописанных препаратов, регулярное измерение АД и его стабилизация при скачках. Снижение массы тела имеет первоочередное значение. Постоянное посещение врача поможет избежать тяжелого состояния.</span></p>",
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            },
            "code": "J86",
            "name": "Пиоторакс",
            "icd_name": "Пиоторакс",
            "gender": 0,
            "age_min": 0,
            "age_max": 100,
            "cause": [
                3,
                1,
                2
            ],
            "periodicity": 1,
            "slug": "j86_piotoraks",
            "lead": "Нарушение здоровья, относящееся к группе гнойные и некротические состояния нижних дыхательных путей",
            "description": "Пиоторакс - скопление гноя или жидкости с биологическими признаками инфицирования в плевральной полости с вовлечением в воспалительный процесс париетальной и висцеральной плевры и вторичным сдавлением легочной ткани.  ",
            "etiology": "<p>Чаще эмпиемы плевры являются вторичными по своему происхождению и развиваются при непосредственном переходе гнойного процесса с легкого, средостения, перикарда, грудной стенки, поддиафрагмального пространства. </p>\r\n<p>Чаще всего эмпиема плевры возникает при острых или хронических инфекционных легочных процессах: пневмонии, бронхоэктазах, абсцессе легкого, гангрене легкого, туберкулезе, нагноившейся кисте легкого и др. В ряде случаев эмпиемой плевры осложняется течение спонтанного пневмоторакса, экссудативного плеврита, медиастинита, перикардита, остеомиелита ребер и позвоночника, поддиафрагмального абсцесса, абсцесса печени, острого панкреатита. Метастатические эмпиемы плевры обусловлены распространением инфекции гематогенным или лимфогенным путем из отдаленных гнойных очагов (например, при остром аппендиците, ангине, сепсисе и др.). </p>\r\n<p>Посттравматический гнойный плеврит, как правило, связан с травмами легкого, ранениями грудной клетки, разрывом пищевода. Послеоперационная эмпиема плевры может возникать после резекции легких, пищевода, кардиохирургических и других операций на органах грудной полости.  </p>",
            "pathogenesis": "<p>Первая стадия протекает с образованием в плевральной полости серозного выпота. Своевременно начатая антибактериальная терапия позволяет подавить экссудативные процессы и способствует спонтанной резорбции жидкости. В случае неадекватно подобранной противомикробной терапии в плевральном экссудате начинается рост и размножение гноеродной флоры, что приводит к переходу плеврита в следующую стадию - фибринозно-гнойную. </p>\r\n<p>В этой фазе эмпиемы плевры вследствие увеличения количества бактерий, детрита (продукт распада тканей), лейкоцитов экссудат становится мутным, приобретая гнойный характер. На поверхности висцеральной и париетальной плевры образуется фибринозный налет, возникают рыхлые, а затем плотные спайки между листками плевры. Сращения образуют ограниченные внутриплевральные осумкования, содержащие скопление густого гноя. </p>\r\n<p>В стадии фиброзной организации происходит образование плотных плевральных спаек, которые, как панцирь, сковывают поджатое легкое. Со временем нефункционирующая легочная ткань подвергается фиброзным изменениям с развитием цирроза легкого.  </p>",
            "diagnostics": "<p> Лабораторные методы исследования крови и мочи.  </p>\r\n<p>Общеклинические анализы крови и мочи, биохимические анализы крови направлены на выявление признаков интоксикации и гнойного воспаления, органной недостаточности. </p>\r\n<p> Лабораторное исследование мокроты.  </p>\r\n<p>Бактериоскопическое исследование мокроты позволяет ориентировочно судить об этиологии деструкции </p>\r\n<p>Обзорная рентгенография органов грудной клетки. </p>\r\n<p>Она позволяет установить локализацию патологического процесса, определить степень отграничения экссудата (свободный или осумкованный), а также относительно точно определить его объем. </p>\r\n<p>Компьютерная томография органов грудной клетки.  </p>\r\n<p>Позволяет убедительно уставить характер поражения легкого, которое стало причиной эмпиемы плевры, определить локализацию осумкований (для последующего выбора способа дренирования), определить наличие свища культи бронха </p>\r\n<p>Ультразвуковое исследование плевральных полостей.  </p>\r\n<p>Необходимо для определения точки для безопасного и адекватного дренирования плевральной полости в случае наличия осумкований.  </p>\r\n<p>Диагностическая пункция плевральной полости.  </p>\r\n<p>Является окончательная методом верификация диагноза. Получение гнойного содержимого плевральной полости позволяет считать предположительный диагноз эмпиемы плевры абсолютно достоверным.   </p>\r\n<p> Фибробронхоскопия.  </p>\r\n<p>Преследует несколько целей: определить дренирующий бронх, если причиной эмпиемы является абсцесс легкого; исключить центральный рак легкого, нередко вызывающий канцероматоз плевры (раковый плеврит), трансформирующийся в эмпиему плевры при инфицировании экссудата; исследовать промывные воды бронхов для установления микробиологического агента и подбора рациональной антибактериальной терапии; провести санацию трахеобронхиального дерева при наличии деструктивного процесса в легких.   </p>",
            "treatment": "<p>При установлении диагноза эмпиемы плевры требуется госпитализация пациента в специализированное торакальное хирургическое отделение.  </p>\r\n<p>В лечении эмпиемы плевры используются как консервативные, так и оперативные методы, которые применяются параллельно друг другу, начиная с самого раннего этапа лечения.  </p>\r\n<p>Большое значение придается раннему и эффективному опорожнению плевральной полости от гнойного содержимого. Это достигается с помощью дренирования плевральной полости, вакуум-аспирации гноя, плеврального лаважа, введения антибиотиков и протеолитических ферментов, лечебных бронхоскопий. Эвакуация гнойного экссудата способствует уменьшению интоксикации, расправлению легкого, спаиванию листков плевры и ликвидации полости эмпиемы плевры. </p>\r\n<p>Одновременно с местным введением противомикробных средств назначается массивная системная антибиотикотерапия. Проводится дезинтоксикационная, иммунокорригирующая терапия, витаминотерапия, переливание белковых препаратов (плазмы крови, альбумина, гидролизатов), растворов глюкозы, электролитов. </p>\r\n<p>В период рассасывания экссудата назначаются процедуры, предотвращающие об­разование плевральных сращений - дыхательная гимнастика, ЛФК, ультразвук, классический, перкуторный и вибрационный массажгрудной клетки. </p>\r\n<p>При формировании хронической эмпиемы плевры показано хирургическое лечение. При этом может выполняться торакостомия (открытое дренирование), плеврэктомия с декортикацией легкого, интраплевральная торакопластика, закрытие бронхоплеврального свища, различные варианты резекции легкого. </p>",
            "prevention": "<p>Профилактика эмпиемы плевры заключается в своевременной антибиотикотерапии легочных и внелегочных инфекционных процессов, соблюдении тща­тельной асептики при хирургических вмешательствах на грудной полости, достижении быстрого расправления легкого в послеопераци­онном периоде, повышении общей резистентности организма.</p>",
            "clinical_picture": "<p>Клиника пиоторакса включает: </p>\r\n<ul>\r\n<li>Боль в грудной клетке со стороны патологического процесса, усиливающаяся на высоте вдоха, при кашле, изменении положения тела в пространстве.  </li>\r\n<li>Принятие положения лежа на больном боку, способствующего уменьшению интенсивности болевых ощущений.  </li>\r\n<li>Частое принятие положения под названием ортопноэ, сидя с развернутым плечевым поясом, опираясь руками на постель.  </li>\r\n<li>Выраженная одышка в покое, синюшность мочек ушей, губ и кистей рук.  </li>\r\n<li>Повышение температуры тела до 38–39 °C.  </li>\r\n<li>Тахикардия (учащение пульса свыше 90 в минуту). </li>\r\n</ul>\r\n<p>Для хронической эмпиемы характерно формирование симптома барабанных палочек. При осмотре выявляют деформацию грудной клетки на стороне эмпие­мы вследствие сужения межреберных промежутков. У детей развивается сколиоз с выпуклостью в здоровую сторону. Дыхательные шумы над полостью хронической эмпиемы плевры не выслушиваются.  </p>",
            "image": null,
            "image_alt": null,
            "standard_type": 3,
            "danger": 51,
            "published": 2,
            "parent": null,
            "block_rubric": 107,
            "standards": []
        },
        {
            "id": 6635,
            "symptoms": [],
            "alternative_names": [],
            "complications": [],
            "medicine_branches": [
                {
                    "id": 37,
                    "disease_count": null,
                    "name": "пульмонология",
                    "code": "B37",
                    "branch_medicine_code": "037",
                    "slug": "pulmonologiya",
                    "lead": "Область медицины, включающая в себя лечение 145 заболеваний. В 181 клинике России оказывается помощь по этому направлению медицины.",
                    "image": null
                },
                {
                    "id": 16,
                    "disease_count": null,
                    "name": "клиническая лабораторная диагностика",
                    "code": "B16",
                    "branch_medicine_code": "016",
                    "slug": "klinicheskaya_laboratornaya_diagnostika",
                    "lead": "Область медицины, включающая в себя лечение 2214 заболеваний. В 886 клиниках России оказывается помощь по этому направлению медицины.",
                    "image": null
                },
                {
                    "id": 15,
                    "disease_count": null,
                    "name": "кардиология, детская кардиология",
                    "code": "B15",
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                            "name": "Боль загрудинная при кашле"
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                            "name": "Боль загрудинная справа"
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            },
            "code": "J93",
            "name": "Пневмоторакс",
            "icd_name": "Пневмоторакс",
            "gender": 0,
            "age_min": 0,
            "age_max": 100,
            "cause": [
                3,
                1
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            "periodicity": 1,
            "slug": "j93_pnevmotoraks",
            "lead": "Нарушение здоровья, относящееся к группе другие болезни плевры",
            "description": "Пневмотораксом называют проникновение воздуха в полость плевры, из-за чего возникает частичный (неполный) или абсолютный коллапс легкого, герметичность которого нарушилась. Патология бывает одно- или двухсторонней, травматичной этиологии или спонтанно возникающая. ",
            "etiology": "<p>К причинам развития пневмоторакса относят: </p>\r\n<ul>\r\n<li>закрытая травма грудной клетки: повреждение лёгкого отломками рёбер; </li>\r\n<li>открытая травма грудной клетки: проникающие ранения; </li>\r\n<li>ятрогенные повреждения (осложнение после лечебного или диагностического вмешательства) </li>\r\n<li>неспецифический пневмоторакс: разрыв булл (очаговая буллезная эмфизема), кист, прорыв абсцесса лёгкого в плевральную полость (пиопневмоторакс), спонтанный разрыв пищевода; </li>\r\n<li>туберкулёзный пневмоторакс: разрыв каверны, прорывы казеозных очагов; </li>\r\n<li>искусственный пневмоторакс накладывают с лечебной целью при туберкулёзе лёгких, с диагностической для торакоскопии, для дифференциальной диагностики образований грудной стенки. </li>\r\n</ul>\r\n<p>Причинами первичного спонтанного пневмоторакса могут быть: </p>\r\n<ul>\r\n<li>генетически обусловленная слабость плевры, при которой для её разрыва достаточно смеха, приступа кашля, физического напряжения; </li>\r\n<li>врожденная нехватка фермента альфа-1-антитрипсина, вызывающая патологические процессы в легких; </li>\r\n<li>путешествие на самолете (перепады давления), дайвинг, ныряние. </li>\r\n</ul>\r\n<p>Вторичный спонтанный пневмоторакс развивается в связи с легочной патологией: </p>\r\n<ul>\r\n<li>болезни легких, травмирующие соединительную ткань (саркоидоз, лимфангиолейомиоматоз, идиопатический пневмосклероз, туберозный склероз); </li>\r\n<li>злокачественные новообразования (рак легкого, саркома); </li>\r\n<li>болезни дыхательных путей (муковисцидоз, бронхиальная астма в тяжелой форме, ХОБЛ); </li>\r\n<li>инфекционные болезни легких (абсцесс легкого, туберкулез, пневмония на фоне ВИЧ); </li>\r\n<li>системные болезни соединительной ткани, включающие поражение легких (дерматомиозит, ревматоидный артрит, системная склеродермия, полимиозит, синдром Марфана). </li>\r\n</ul>",
            "pathogenesis": "<p>Воздух или газ может попадать в плевральную полость снаружи (при открытом повреждении грудной клетки и сообщении с внешней средой) или из внутренних органов (например, при травматическом разрыве лёгкого при закрытой травме, либо при разрыве эмфизематозных пузырей, «булл», при минимальной травме или кашле, спонтанный пневмоторакс). В норме лёгкое расправлено за счёт того, что в плевральной полости, как правило, давление меньше, чем в самом легком. Поэтому при попадании туда воздуха лёгкое спадается. </p>\r\n<p>Различают откры­тый, закрытый и клапанный пневмоторакс. При открытом полость плевры сообщается с просветом бронхов, при закрытом дефект в плев­ре закрывается в результате коллапса легкого, воспаления и выпаде­ния фибрина. При клапанном пневмотораксе воздух входит во время вдоха в плевральную полость, но на выдохе дефект закрывается. В результате нарастает внутриплевральное давление с развитием на­пряженного пневмоторакса, смещением органов средостения в про­тивоположную сторону, нарастанием дыхательной и сердечной недо­статочности. </p>",
            "diagnostics": "<p>При анализе газов артериальной крови гипоксемия (снижение парциального давления кислорода крови) наблюдается у 75 % больных с пневмотораксом. </p>\r\n<p>Для подтверждения диагноза необходимо проведение рентгенографии грудной клетки (оптимальная проекция — переднезадняя, при вертикальном положении больного. Для диагностики небольших по размеру пневмотораксов КТ является более надежным методом по сравнению с рентгенографией. </p>",
            "treatment": "<p>Первая помощь при открыом пневмотораксе - перевести его в закрытый путем наложения стерильной повязки на открытую рану грудной клетки.  При наличии клапанного пневмоторакса необходимо срочное проведение плевральной пункции с целью удаления свободного газа, расправления легкого и устранения смещения органов средостения. </p>\r\n<p>Лечение пневмоторакса заключается в его ликвидации путём отсасывания воздуха из плевральной полости и восстановления в ней отрицательного давления.  </p>\r\n<p>При закрытом пневмотораксе без действующего сообщения с лёгким достаточно пункционной аспирации газа из плевральной полости при помощи набора для ликвидации пневмоторакса в асептических условиях операционной. Если аспирация иглой оказывается неэффективной, это свидетельствует о поступлении воздуха из ткани лёгкого. В таких случаях выполняют герметичное дренирование плевральной полости («дренаж по Бюлау»), либо создают систему активной аспирации, в том числе с применением электровакуумных приборов.  </p>\r\n<p>Открытый пневмоторакс требует первоначальной торакотомии или торакоскопии, ревизии органов плевральной полости, устранения повреждений легочной паренхимы, а затем дренирования плевральной полости и ушивания последней. </p>\r\n<p>При наличии неразорвавшихся булл принимается решение об удалении сегмента или доли легкого и плевродеза (формирование сращений между листками плевры) для недопущения возникновения пневмоторакса. </p>",
            "prevention": "<p>Рекомендованная для пневмоторакса профилактика включает в себя: </p>\r\n<ul>\r\n<li>Своевременное лечение заболевания лёгких; </li>\r\n<li>Предотвращение травм грудной клетки; </li>\r\n<li>Профилактика повторных пневмотораксов.</li>\r\n</ul>\r\n<p> </p>",
            "clinical_picture": "<p>При возникновении пневмоторакса наблюдается: </p>\r\n<ul>\r\n<li>Резкая, колющего характера, сильно ощутимая болезненность в районе грудной клетки с иррадиацией в брюшину (в область кишечника), шею, плечевой пояс; </li>\r\n<li>Нехватка воздуха;</li>\r\n<li>Неполноценное дыхание, кашель;</li>\r\n<li>Учащение, поверхностность дыхательных движений;</li>\r\n<li>Цианоз кожного покрова;</li>\r\n<li>Бледность лица и верхней части туловища;</li>\r\n<li>Выпирание межреберного пространства над пораженным легким;</li>\r\n<li>Отставание в респираторном акте половины грудной полости со стороны предполагаемой патологии;</li>\r\n<li>Беспокойство, боязнь смерти;</li>\r\n<li>Вынужденное положение тела (на больном боку лежа). </li>\r\n</ul>\r\n<p>Пациент с открытым пневмотораксом принимает вынужденное положение, лежа на поврежденной стороне и плотно зажимая рану. Воздух засасывается в рану с шумом, из раны выделяется пенистая кровь с примесью воздуха, экскурсия грудной клетки асимметрична (пораженная сторона отстает при дыхании). </p>\r\n<p>Спустя несколько часов интенсивность боли и одышки ослабевают: боль беспокоит в момент глубокого вдоха, одышка проявляется при физическом усилии. Возможно развитие подкожной или медиастинальной эмфиземы – выход воздуха в подкожную клетчатку лица, шеи, грудной клетки или средостения, сопровождающийся вздутием и характерным хрустом при пальпации. Аускультативно на стороне пневмоторакса дыхание ослаблено или не выслушивается. </p>",
            "image": null,
            "image_alt": null,
            "standard_type": 3,
            "danger": 1,
            "published": 2,
            "parent": null,
            "block_rubric": 108,
            "standards": [
                5154
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        },
        {
            "id": 6639,
            "symptoms": [],
            "alternative_names": [],
            "complications": [],
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                    "name": "пульмонология",
                    "code": "B37",
                    "branch_medicine_code": "037",
                    "slug": "pulmonologiya",
                    "lead": "Область медицины, включающая в себя лечение 145 заболеваний. В 181 клинике России оказывается помощь по этому направлению медицины.",
                    "image": null
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                    "code": "B16",
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                    "slug": "klinicheskaya_laboratornaya_diagnostika",
                    "lead": "Область медицины, включающая в себя лечение 2214 заболеваний. В 886 клиниках России оказывается помощь по этому направлению медицины.",
                    "image": null
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                {
                    "id": 15,
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                    "lead": "Область медицины, включающая в себя лечение 634 заболеваний. В 731 клинике России оказывается помощь по этому направлению медицины.",
                    "image": null
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