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"code": "R04",
"name": "Кровотечение из дыхательных путей",
"icd_name": "Кровотечение из дыхательных путей",
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"age_min": 0,
"age_max": 100,
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3,
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"slug": "r04_krovotechenie_iz_dyhatelnyh_putey",
"lead": "Нарушение здоровья, относящееся к группе симптомы и признаки, относящиеся к системам кровообращения и дыхания",
"description": "Кровотечение из верхних дыхательных путей— это опасное осложнение различных заболеваний органов дыхания. Сопровождается истечением крови из бронхиальных или легочных сосудов, сосудов полости носа и выделением ее из дыхательных путей.",
"etiology": "<p>Наиболее распространённые причины носового кровотечения:</p>\r\n<ul>\r\n<li>Травманоса;</li>\r\n<li>Инородные тела;</li>\r\n<li>Воспалительные процессы.</li>\r\n</ul>\r\n<p>Другие возможные причины:</p>\r\n<ul>\r\n<li>Анатомические деформации;</li>\r\n<li>Вдыхание наркотиков(особенно кокаина);</li>\r\n<li>Опухоли полости носа (назофарингеальная карциномаи др.);</li>\r\n<li>Низкая относительная влажность вдыхаемого воздуха;</li>\r\n<li>Применение носового кислородного катетера;</li>\r\n<li>Применение назального спрея;</li>\r\n<li>Баротравма;</li>\r\n<li>Оперативное вмешательство (пластика носовой перегородки и др.).</li>\r\n</ul>\r\n<p>Кровотечения из дыхательных путей могут вызывать также:</p>\r\n<ul>\r\n<li>болезни трахеи и бронхов: бронхоэктазия, бронхит, острый ларинготрахеит, опухоли; болезни легких: пневмонии, инфаркт легкого, туберкулез легкого, рак легкого, легочное нагноение, паразитарные болезни (эхинококкоз легкого, аскаридоз);</li>\r\n<li>профессиональные болезни легких; синдром Гудпасчера; идиопатический гемосидероз легких, эмфизема легких;</li>\r\n<li>травмы, груди, острое повышение внутригрудного давления; психоэмоциональное перенапряжение; перегревание под солнцем; проявление истерии;</li>\r\n<li>системные заболевания (красная волчанка, васкулиты, саркоидоз, лейкозы); уремия; холемия; передозировка антикоагулянтов, антиагрегантов;</li>\r\n<li>инфекционные заболевания: грипп, корь, коклюш, геморрагическая лихорадка, легкая форма чумы;</li>\r\n</ul>\r\n<p>Нарушение свертываемости крови при длительном и неадекватном приеме антикоагулянтов (препараты, разжижающие кровь).</p>\r\n<p> </p>",
"pathogenesis": "<p>Причинами кровотечений из дыхательных путей могут быть:</p>\r\n<ul>\r\n<li>повреждение кровеносного сосуда (в т.ч. при травме)</li>\r\n<li>разъедание стенки (аррозия) сосуда: бронхоэктазы, опухоли, каверны;</li>\r\n<li>разрыв сосуда (при артериовенозных аневризмах, телеангиэктазии);</li>\r\n<li>воспаление сосудов – артерииты;</li>\r\n<li>излияние крови в альвеолы из бронхиальной артерии (при инфаркте легкого);</li>\r\n<li>диапедезные кровотечения (тромбоцитопенический синдром, застойное полнокровие легочных сосудов).</li>\r\n</ul>",
"diagnostics": "<p>Для определения локализации источника носового кровотечения (переднее или заднее кровотечение) проводится осмотр пациента, фарингоскопия и передняя риноскопия.</p>\r\n<p>Локализацию источника кровотечения можно установить при рентгенологическом исследовании (по характеру поражения легких), более точно — при трахеобронхоскопии.</p>\r\n<p>Лабораторная диагностика включает: коагулограмму (исследование крови на ее способность к свертыванию); анализ мокроты (выявление микобактерий туберкулеза).</p>\r\n<p>Диагностика включает также:</p>\r\n<ul>\r\n<li>рентгенографию органов грудной клетки;</li>\r\n<li>компьютерную томографию (КТ) органов грудной клетки;</li>\r\n<li>ангиопульмонографию – исследование сосудов легких с помощью вводимого в сосуды контрастного вещества (выделяется на снимках при проведении рентгенографии и позволяет определить наличие патологических изменений в сосудах легких);</li>\r\n<li>биопсия – взятие кусочка легочной ткани для исследования на клеточный состав.</li>\r\n</ul>",
"treatment": "<p>При носовом кровотечении придать сидячее положение, успокоить больного. Прижать крылья носа к носовой перегородке на 10-15 мин, холод на переносицу. Ввести в носовые ходы турунды, смоченные 3% раствором перекиси водорода, можно использовать гемостатическую губку. При отсутствии эффекта проводится передняя тампонада носа.</p>\r\n<p>При легочном кровотечении проводится:</p>\r\n<ul>\r\n<li>Обеспечение больному полусидячего положения с опущенными вниз ногами.</li>\r\n<li>Удаление крови из дыхательных путей (отсасывание с помощью специальных аппаратов).</li>\r\n<li>Введение кровоостанавливающих препаратов.</li>\r\n<li>Лечебная бронхоскопия – метод, позволяющий осмотреть дыхательные пути изнутри, определить источник кровотечения и произвести манипуляции по остановке кровотечения: закупорка кровоточащего сосуда с помощью специальных средств. </li>\r\n<li>Оперативное лечение – открытая операция на легких с ушиванием кровоточащего сосуда или удалением части легкого.</li>\r\n<li>При большом объеме потерянной крови – переливание крови и ее компонентов, введение препаратов, восстанавливающих объем циркулирующей крови.</li>\r\n<li>Антибиотики – для профилактики присоединения инфекции.</li>\r\n<li>Лечение основного заболевания, приведшего к легочному кровотечению.</li>\r\n</ul>",
"prevention": "<p>Профилактические мероприятия включают:</p>\r\n<ul>\r\n<li>своевременное выявление и проведение адекватного лечения болезней дыхательной и сердечно-сосудистой систем, а также системных заболеваний;</li>\r\n<li>периодический контроль состояния свертывающей системы крови в случае применения антикоагулянтов (лекарственных препаратов, разжижающих кровь);</li>\r\n<li>избегание травм грудной клетки и носа.</li>\r\n</ul>\r\n<p> </p>",
"clinical_picture": "<p>Непосредственным признаком носового кровотечения является истечение крови из полости носа наружу или внутрь носоглотки. В последнем случае кровь стекает в ротоглотку, где и обнаруживается при фарингскопии.</p>\r\n<p>Могут возникнуть головокружение, шум в ушах, жажда, общая слабость, сердцебиение. В некоторых случаях может отмечаться незначительная бледность кожи.</p>\r\n<p>Кровопотеря средней степени тяжести сопровождается выраженным головокружением, падением артериального давления, акроцианозом, тахикардией и одышкой. При тяжелой кровопотере развивается геморрагический шок. Пациент заторможен, возможна потеря сознания. Во время осмотра выявляют нитевидный пульс, выраженную тахикардию, резкое падение АД.</p>\r\n<p>Симптомы легочного кровотечения:</p>\r\n<ul>\r\n<li>выделение при кашле алой крови или ее сгустков из дыхательных путей, часть выделенной крови пенистая;</li>\r\n<li>кожа покрывается холодным липким потом, бледная;</li>\r\n<li>одышка;</li>\r\n<li>учащенное сердцебиение;</li>\r\n<li>снижение артериального давления;</li>\r\n<li>чувство страха;</li>\r\n<li>шум в ушах;</li>\r\n<li>головокружение;</li>\r\n<li>при массивном кровотечении – обморок.</li>\r\n</ul>\r\n<p>При кровохарканьи наблюдается выделение (откашливание) из бронхов и легких крови в виде прожилок и примеси крови в мокроте, окрашенных кровью плевков. Объем выделяемой крови не превышает 50 мл в сутки.</p>",
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},
"code": "R04.0",
"name": "Носовое кровотечение",
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"lead": "патологическое состояние, характеризующееся выделением крови из носовой полости",
"description": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Носовое кровотечение — распространённый симптом ЛОР-заболеваний, который возникает при нарушении целостности сосудов, расположенных в полости носа, носоглотки, околоносовых пазухах, а также при повреждении верхней стенки полости носа.</span></p>",
"etiology": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Причины подразделяются на местные и общие. К местным относятся процессы, происходящие непосредственно внутри носовой полости:</span></p>\r\n<ul style=\"margin-top: 0; margin-bottom: 0; padding-inline-start: 48px;\">\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Любые травмы носа, его слизистой оболочки и внутриносовых структур, в том числе травмы, вызванные хирургическим или другим медицинским вмешательством и инородными телами, повреждения головы.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Дистрофические изменения слизистой оболочки: искривление носовой перегородки, ринит атрофической формы.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Новообразования внутри носоглотки: гранулемы, опухоли, ангиомы, саркомы, папилломы и т.д.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Воспалительные процессы, из-за возникает гиперемия (переполненность кровью) слизистой оболочки: синуситы, риниты.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Сухость слизистой оболочки носоглотки из-за недостаточной влажности воздуха.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Вдыхание веществ, раздражающих слизистую оболочку полости носа.</span></li>\r\n</ul>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Общие причины носового кровотечения:</span></p>\r\n<ul style=\"margin-top: 0; margin-bottom: 0; padding-inline-start: 48px;\">\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Сердечно-сосудистые патологии: гипертоническая болезнь, атеросклероз, пороки сердца и сосудов.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Значительное повышение температуры тела вследствие перегрева организма, солнечного удара, инфекций.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Наследственные и приобретенные заболевания крови (особенно связанные с нарушением ее свертываемости).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Интоксикации организма (включая алкогольные).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Недостаток или избыток витаминов в организме.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Передозировка антикоагулянтов (препаратов, разжижающих кровь).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Эндокринные патологии: гипотиреоз (недостаток гормонов щитовидной железы), гипоэстрогения (дефицит женских половых гормонов – эстрогенов).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Заболевания печени и почек.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Физическое перенапряжение.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Нарушения гормонального фона или гормональная естественная перестройка организма (например, носовые кровотечения часто наблюдаются у беременных и у подростков в период полового созревания).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Изменения в организме, возникшие из-за перепадов барометрического давления (возникают у людей, занимающихся подводным плаванием или альпинизмом, совершающих перелеты на самолете или вертолете).</span></li>\r\n</ul>",
"pathogenesis": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">В носовой полости расположены анастомозы двух сосудистых бассейнов: мозгового и внемозгового. Тонус мозговых сосудов относительно устойчивый, а внемозговых — довольно лабильный. В области анастомозов в норме происходит уравновешивание внутрисосудистого давления с обеих сторон. Действие провоцирующих факторов приводит к повышению тонуса внемозговых сосудов, нарушению податливости сосудистой стенки и ее разрыву.</span></p>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Дополнительными триггерами носового кровотечения являются расстройства гемостаза и микроциркуляции. Самая податливая область — зона Киссельбаха (передне-наружная часть носовой перегородки), она является источником 90% носовых кровотечений. Около 10% случаев происходит из сосудов боковой стенки, задней части перегородки.</span></p>",
"diagnostics": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Диагностика осуществляется в несколько этапов:</span></p>\r\n<ul style=\"margin-top: 0; margin-bottom: 0; padding-inline-start: 48px;\">\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Сбор анамнеза, который в большинстве случаев позволяет определить причину кровотечения (травма, артериальная гипертензия и т.д.).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Визуальный осмотр носа и его полости, в ходе которого можно установить источник патологии.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Измерение артериального давления.</span></li>\r\n</ul>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Могут быть назначены дополнительные исследования:</span></p>\r\n<ul style=\"margin-top: 0; margin-bottom: 0; padding-inline-start: 48px;\">\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Общий анализ крови.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Коагулограмма (анализ на свертываемость крови).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Пробы на механическую устойчивость капилляров.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Исследование системы гемостаза.</span></li>\r\n</ul>",
"treatment": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Первая помощь</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">В стационарном лечении нуждаются дети с непрекращающимся кровотечением, ухудшением состояния, данными за травму, отягощенным соматическим анамнезом. Первоочередные действия по остановке кровотечения у ребенка проводятся на догоспитальном этапе:</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Придание правильного положения. Ребенка следует посадить, чтобы голова была выше туловища, слегка наклонена вперед. Кровь должна стекать в лоток. Необходимо объяснить принципы правильного дыхания: глубокие вдохи через нос, выдохи через рот. Отсмаркивание при НК недопустимо.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Проведение гемостатических мероприятий. К спинке носа прикладывают холод, носовой ход зажимают пальцем на 5-10 минут. При неэффективности в преддверие носа помещают ватный тампон, смоченный 3% раствором перекиси водорода или детскими сосудосуживающими назальными каплями. Тампон может быть заменен гемостатической губкой.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Отсутствие эффекта от базовой помощи в течение 20 минут — показание для госпитализации в ЛОР-отделение стационара. Транспортировка ребенка осуществляется в положении сидя либо лежа на животе. Во время транспортировки вышеописанные процедуры продолжаются.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Тампонада носа</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Окончательная остановка носового кровотечения в стационаре предусматривает проведение тампонады. Передняя тампонада представляет собой введение стерильной марлевой турунды через передний носовой ход. Турунда предварительно смачивается гемостатическим раствором. После проведения локальной анестезии в полость носа вводится марлевый тампон длиною 70 см, шириной 1 см. Тампон укладывается по типу «гармошки», плотно заполняя необходимую половину носа.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">При неэффективности метода осуществляется задняя тампонада. Ватно-марлевый тампон готовят из стерильного материала, прошивают в виде тюка, размер которого условно равен размеру ногтевой фаланги большого пальца руки данного ребенка. Через носовой ход в ротовую полость проводится тонкий катетер. К внутреннему концу катетера привязывают нити тампона, внешнюю часть подтягивают наружу, пока тампон не закроет плотно носовые хоаны. Длительность стояния турунды достигает 2-5 суток.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Хирургическое лечение</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Оперативное вмешательство показано при неэффективности тампонирования, при рецидивирующих носовых кровотечениях. При точной идентификации кровоточащего сосуда проводится эндоскопическая электрокоагуляция. При кровотечении из зоны Киссельбаха производится отслойка слизистой оболочки с последующей установкой тампона.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Хирургическим методом остановки тяжелых носовых кровотечений из решетчатых артерий является трансмаксиллярная тампонада решетчатого лабиринта. В случае упорного кровотечения из бассейна наружной сонной артерии проводится клипирование челюстной артерии или эмболизация сонной.</span></p>",
"prevention": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Для предотвращения носового кровотечения врачи рекомендуют соблюдать такие правила:</span></p>\r\n<p> </p>\r\n<ul style=\"margin-top: 0; margin-bottom: 0; padding-inline-start: 48px;\">\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">увлажнять воздух в помещении;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">при сильной сухости в носу увлажнять слизистую оболочку;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">избегать травм головы и носа;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">стараться не вдыхать аллергены и другие раздражители;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">своевременно проводить профилактику инфекционных заболеваний;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">контролировать артериальное давление;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">внести в рацион питания больше ягод, свежих овощей и фруктов;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">чаще гулять на улице после дождя;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">при приеме медикаментов, влияющих на кровь, регулярно контролировать ее свертываемость.</span></p>\r\n</li>\r\n</ul>",
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"code": "R04",
"name": "Кровотечение из дыхательных путей",
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"lead": "Нарушение здоровья, относящееся к группе симптомы и признаки, относящиеся к системам кровообращения и дыхания",
"description": "Кровотечение из верхних дыхательных путей— это опасное осложнение различных заболеваний органов дыхания. Сопровождается истечением крови из бронхиальных или легочных сосудов, сосудов полости носа и выделением ее из дыхательных путей.",
"etiology": "<p>Наиболее распространённые причины носового кровотечения:</p>\r\n<ul>\r\n<li>Травманоса;</li>\r\n<li>Инородные тела;</li>\r\n<li>Воспалительные процессы.</li>\r\n</ul>\r\n<p>Другие возможные причины:</p>\r\n<ul>\r\n<li>Анатомические деформации;</li>\r\n<li>Вдыхание наркотиков(особенно кокаина);</li>\r\n<li>Опухоли полости носа (назофарингеальная карциномаи др.);</li>\r\n<li>Низкая относительная влажность вдыхаемого воздуха;</li>\r\n<li>Применение носового кислородного катетера;</li>\r\n<li>Применение назального спрея;</li>\r\n<li>Баротравма;</li>\r\n<li>Оперативное вмешательство (пластика носовой перегородки и др.).</li>\r\n</ul>\r\n<p>Кровотечения из дыхательных путей могут вызывать также:</p>\r\n<ul>\r\n<li>болезни трахеи и бронхов: бронхоэктазия, бронхит, острый ларинготрахеит, опухоли; болезни легких: пневмонии, инфаркт легкого, туберкулез легкого, рак легкого, легочное нагноение, паразитарные болезни (эхинококкоз легкого, аскаридоз);</li>\r\n<li>профессиональные болезни легких; синдром Гудпасчера; идиопатический гемосидероз легких, эмфизема легких;</li>\r\n<li>травмы, груди, острое повышение внутригрудного давления; психоэмоциональное перенапряжение; перегревание под солнцем; проявление истерии;</li>\r\n<li>системные заболевания (красная волчанка, васкулиты, саркоидоз, лейкозы); уремия; холемия; передозировка антикоагулянтов, антиагрегантов;</li>\r\n<li>инфекционные заболевания: грипп, корь, коклюш, геморрагическая лихорадка, легкая форма чумы;</li>\r\n</ul>\r\n<p>Нарушение свертываемости крови при длительном и неадекватном приеме антикоагулянтов (препараты, разжижающие кровь).</p>\r\n<p> </p>",
"pathogenesis": "<p>Причинами кровотечений из дыхательных путей могут быть:</p>\r\n<ul>\r\n<li>повреждение кровеносного сосуда (в т.ч. при травме)</li>\r\n<li>разъедание стенки (аррозия) сосуда: бронхоэктазы, опухоли, каверны;</li>\r\n<li>разрыв сосуда (при артериовенозных аневризмах, телеангиэктазии);</li>\r\n<li>воспаление сосудов – артерииты;</li>\r\n<li>излияние крови в альвеолы из бронхиальной артерии (при инфаркте легкого);</li>\r\n<li>диапедезные кровотечения (тромбоцитопенический синдром, застойное полнокровие легочных сосудов).</li>\r\n</ul>",
"diagnostics": "<p>Для определения локализации источника носового кровотечения (переднее или заднее кровотечение) проводится осмотр пациента, фарингоскопия и передняя риноскопия.</p>\r\n<p>Локализацию источника кровотечения можно установить при рентгенологическом исследовании (по характеру поражения легких), более точно — при трахеобронхоскопии.</p>\r\n<p>Лабораторная диагностика включает: коагулограмму (исследование крови на ее способность к свертыванию); анализ мокроты (выявление микобактерий туберкулеза).</p>\r\n<p>Диагностика включает также:</p>\r\n<ul>\r\n<li>рентгенографию органов грудной клетки;</li>\r\n<li>компьютерную томографию (КТ) органов грудной клетки;</li>\r\n<li>ангиопульмонографию – исследование сосудов легких с помощью вводимого в сосуды контрастного вещества (выделяется на снимках при проведении рентгенографии и позволяет определить наличие патологических изменений в сосудах легких);</li>\r\n<li>биопсия – взятие кусочка легочной ткани для исследования на клеточный состав.</li>\r\n</ul>",
"treatment": "<p>При носовом кровотечении придать сидячее положение, успокоить больного. Прижать крылья носа к носовой перегородке на 10-15 мин, холод на переносицу. Ввести в носовые ходы турунды, смоченные 3% раствором перекиси водорода, можно использовать гемостатическую губку. При отсутствии эффекта проводится передняя тампонада носа.</p>\r\n<p>При легочном кровотечении проводится:</p>\r\n<ul>\r\n<li>Обеспечение больному полусидячего положения с опущенными вниз ногами.</li>\r\n<li>Удаление крови из дыхательных путей (отсасывание с помощью специальных аппаратов).</li>\r\n<li>Введение кровоостанавливающих препаратов.</li>\r\n<li>Лечебная бронхоскопия – метод, позволяющий осмотреть дыхательные пути изнутри, определить источник кровотечения и произвести манипуляции по остановке кровотечения: закупорка кровоточащего сосуда с помощью специальных средств. </li>\r\n<li>Оперативное лечение – открытая операция на легких с ушиванием кровоточащего сосуда или удалением части легкого.</li>\r\n<li>При большом объеме потерянной крови – переливание крови и ее компонентов, введение препаратов, восстанавливающих объем циркулирующей крови.</li>\r\n<li>Антибиотики – для профилактики присоединения инфекции.</li>\r\n<li>Лечение основного заболевания, приведшего к легочному кровотечению.</li>\r\n</ul>",
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"lead": "патологическое состояние, характеризующееся выделением крови из носовой полости",
"description": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Носовое кровотечение — распространённый симптом ЛОР-заболеваний, который возникает при нарушении целостности сосудов, расположенных в полости носа, носоглотки, околоносовых пазухах, а также при повреждении верхней стенки полости носа.</span></p>",
"etiology": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Причины подразделяются на местные и общие. К местным относятся процессы, происходящие непосредственно внутри носовой полости:</span></p>\r\n<ul style=\"margin-top: 0; margin-bottom: 0; padding-inline-start: 48px;\">\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Любые травмы носа, его слизистой оболочки и внутриносовых структур, в том числе травмы, вызванные хирургическим или другим медицинским вмешательством и инородными телами, повреждения головы.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Дистрофические изменения слизистой оболочки: искривление носовой перегородки, ринит атрофической формы.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Новообразования внутри носоглотки: гранулемы, опухоли, ангиомы, саркомы, папилломы и т.д.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Воспалительные процессы, из-за возникает гиперемия (переполненность кровью) слизистой оболочки: синуситы, риниты.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Сухость слизистой оболочки носоглотки из-за недостаточной влажности воздуха.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Вдыхание веществ, раздражающих слизистую оболочку полости носа.</span></li>\r\n</ul>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Общие причины носового кровотечения:</span></p>\r\n<ul style=\"margin-top: 0; margin-bottom: 0; padding-inline-start: 48px;\">\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Сердечно-сосудистые патологии: гипертоническая болезнь, атеросклероз, пороки сердца и сосудов.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Значительное повышение температуры тела вследствие перегрева организма, солнечного удара, инфекций.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Наследственные и приобретенные заболевания крови (особенно связанные с нарушением ее свертываемости).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Интоксикации организма (включая алкогольные).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Недостаток или избыток витаминов в организме.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Передозировка антикоагулянтов (препаратов, разжижающих кровь).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Эндокринные патологии: гипотиреоз (недостаток гормонов щитовидной железы), гипоэстрогения (дефицит женских половых гормонов – эстрогенов).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Заболевания печени и почек.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Физическое перенапряжение.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Нарушения гормонального фона или гормональная естественная перестройка организма (например, носовые кровотечения часто наблюдаются у беременных и у подростков в период полового созревания).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Изменения в организме, возникшие из-за перепадов барометрического давления (возникают у людей, занимающихся подводным плаванием или альпинизмом, совершающих перелеты на самолете или вертолете).</span></li>\r\n</ul>",
"pathogenesis": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">В носовой полости расположены анастомозы двух сосудистых бассейнов: мозгового и внемозгового. Тонус мозговых сосудов относительно устойчивый, а внемозговых — довольно лабильный. В области анастомозов в норме происходит уравновешивание внутрисосудистого давления с обеих сторон. Действие провоцирующих факторов приводит к повышению тонуса внемозговых сосудов, нарушению податливости сосудистой стенки и ее разрыву.</span></p>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Дополнительными триггерами носового кровотечения являются расстройства гемостаза и микроциркуляции. Самая податливая область — зона Киссельбаха (передне-наружная часть носовой перегородки), она является источником 90% носовых кровотечений. Около 10% случаев происходит из сосудов боковой стенки, задней части перегородки.</span></p>",
"diagnostics": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Диагностика осуществляется в несколько этапов:</span></p>\r\n<ul style=\"margin-top: 0; margin-bottom: 0; padding-inline-start: 48px;\">\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Сбор анамнеза, который в большинстве случаев позволяет определить причину кровотечения (травма, артериальная гипертензия и т.д.).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Визуальный осмотр носа и его полости, в ходе которого можно установить источник патологии.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Измерение артериального давления.</span></li>\r\n</ul>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Могут быть назначены дополнительные исследования:</span></p>\r\n<ul style=\"margin-top: 0; margin-bottom: 0; padding-inline-start: 48px;\">\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Общий анализ крови.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Коагулограмма (анализ на свертываемость крови).</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Пробы на механическую устойчивость капилляров.</span></li>\r\n<li><span style=\"font-size: 7pt; color: #000000; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Исследование системы гемостаза.</span></li>\r\n</ul>",
"treatment": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Первая помощь</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">В стационарном лечении нуждаются дети с непрекращающимся кровотечением, ухудшением состояния, данными за травму, отягощенным соматическим анамнезом. Первоочередные действия по остановке кровотечения у ребенка проводятся на догоспитальном этапе:</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Придание правильного положения. Ребенка следует посадить, чтобы голова была выше туловища, слегка наклонена вперед. Кровь должна стекать в лоток. Необходимо объяснить принципы правильного дыхания: глубокие вдохи через нос, выдохи через рот. Отсмаркивание при НК недопустимо.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Проведение гемостатических мероприятий. К спинке носа прикладывают холод, носовой ход зажимают пальцем на 5-10 минут. При неэффективности в преддверие носа помещают ватный тампон, смоченный 3% раствором перекиси водорода или детскими сосудосуживающими назальными каплями. Тампон может быть заменен гемостатической губкой.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Отсутствие эффекта от базовой помощи в течение 20 минут — показание для госпитализации в ЛОР-отделение стационара. Транспортировка ребенка осуществляется в положении сидя либо лежа на животе. Во время транспортировки вышеописанные процедуры продолжаются.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Тампонада носа</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Окончательная остановка носового кровотечения в стационаре предусматривает проведение тампонады. Передняя тампонада представляет собой введение стерильной марлевой турунды через передний носовой ход. Турунда предварительно смачивается гемостатическим раствором. После проведения локальной анестезии в полость носа вводится марлевый тампон длиною 70 см, шириной 1 см. Тампон укладывается по типу «гармошки», плотно заполняя необходимую половину носа.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">При неэффективности метода осуществляется задняя тампонада. Ватно-марлевый тампон готовят из стерильного материала, прошивают в виде тюка, размер которого условно равен размеру ногтевой фаланги большого пальца руки данного ребенка. Через носовой ход в ротовую полость проводится тонкий катетер. К внутреннему концу катетера привязывают нити тампона, внешнюю часть подтягивают наружу, пока тампон не закроет плотно носовые хоаны. Длительность стояния турунды достигает 2-5 суток.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Хирургическое лечение</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Оперативное вмешательство показано при неэффективности тампонирования, при рецидивирующих носовых кровотечениях. При точной идентификации кровоточащего сосуда проводится эндоскопическая электрокоагуляция. При кровотечении из зоны Киссельбаха производится отслойка слизистой оболочки с последующей установкой тампона.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Хирургическим методом остановки тяжелых носовых кровотечений из решетчатых артерий является трансмаксиллярная тампонада решетчатого лабиринта. В случае упорного кровотечения из бассейна наружной сонной артерии проводится клипирование челюстной артерии или эмболизация сонной.</span></p>",
"prevention": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Для предотвращения носового кровотечения врачи рекомендуют соблюдать такие правила:</span></p>\r\n<p> </p>\r\n<ul style=\"margin-top: 0; margin-bottom: 0; padding-inline-start: 48px;\">\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">увлажнять воздух в помещении;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">при сильной сухости в носу увлажнять слизистую оболочку;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">избегать травм головы и носа;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">стараться не вдыхать аллергены и другие раздражители;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">своевременно проводить профилактику инфекционных заболеваний;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; 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vertical-align: baseline; white-space: pre-wrap;\">внести в рацион питания больше ягод, свежих овощей и фруктов;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">чаще гулять на улице после дождя;</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 6.5pt; font-family: Verdana; color: #2e2d31; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; 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},
"code": "D03",
"name": "Меланома in situ",
"icd_name": "Меланома in situ",
"gender": 0,
"age_min": 15,
"age_max": 100,
"cause": [
3,
0
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"slug": "d03_melanoma_in_situ",
"lead": "Нарушение здоровья, относящееся к группе новообразования in situ",
"description": "Меланома in situ – это злокачественное новообразование кожи, развивающееся из клеток меланоцитов, развивающееся в пределах верхнего слоя кожи - эпидермиса. Чаще всего развивается на открытых участках тела, которые больше всего подвержены ультрафиолетовому облучению.",
"etiology": "<p>К предрасполагающим факторам, способствующим развитию меланомы, относят:</p>\r\n<ul>\r\n<li>инсоляция солнечными лучами кожи;</li>\r\n<li>особенности кожи – белая, с трудом поддается загару, солнечный ожог развивается за 30 минут воздействия ультрафиолетовых лучей;</li>\r\n<li>невусы (родинки) – доброкачественные новообразования на коже, вырабатывающие меланин – кожный пигмент;</li>\r\n<li>травмирование родинок;</li>\r\n<li>генетическая предрасположенность – наличие у родственников старшего поколения меланомы;</li>\r\n<li>перенесенный рак кожи;</li>\r\n<li>предраковое заболевание кожи – пигментная ксеродерма;</li>\r\n<li>пожилой возраст;</li>\r\n<li>расовая принадлежность человека. Согласно статистике ВОЗ, чернокожие в 4 раза реже страдают от меланомы, чем европеоиды;</li>\r\n<li>наличие сопутствующих хронических заболеваний, которые приводят к снижению общего иммунитета человека.</li>\r\n</ul>",
"pathogenesis": "<p>При изучении процессов возникновения и развития меланом кожи следует учитывать, что эта опухоль является уникальной для изучения вопросов ее канцерогенеза, так как более 50% первичных меланом кожи развивается на фоне предсуществующих пигментных невусов, что позволяет расценивать последний как факультативный предрак, и так как наиболее важными экзогенными этиологическими факторами этой опухоли являются УФ-радиация и травма невусов.</p>\r\n<p>Механизм канцерогенного действия УФ-радиации может заключаться в образовании в нормальных клетках высокоактивных свободных химических радикалов. В основе возникновения опухоли лежат процессы повреждения этими радикалами ДНК клетки, нарушение ее нормальной репарации. Последовательность процессов возникновения меланомы кожи под воздействием УФ-радиации можно схематически представить в следующем виде: УФ-радиация- меланобласты, меланоциты или невусные клетки - повреждение ДНК клетки - нарушение дифференцировки клетки - изменение белковой структуры клетки с возникновением новых мембранных антигенов - гипореактивность - бесконечно долгое размножение (опухолевый рост). Вероятно, такой механизм канцерогенеза меланом кожи является наиболее коротким во времени, так как в данном случае отсутствует длительная пролиферация нормальных клеток и тканей. Клиническим подтверждением возможности «включения» этого механизма канцерогенеза является факт более частого возникновения меланом после однократного и интенсивного воздействия УФ-радиации (солнечного ожога).</p>\r\n<p>Напротив, механизм канцерогенного действия травмы предсуществующих пигментных невусов включает в себя пролиферацию тканей в ответ на их повреждение, но сама травма не приводит к развитию опухоли. Доказано, что клетки в состоянии пролиферации обладают повышенной чувствительностью к канцерогенному воздействию и особенно уязвимы, находясь в фазе митотического цикла. Поэтому интенсивное размножение (пролиферация) клеток может привести к их неопластической трансформации. Последовательность процессов возникновения меланом кожи в результате травмы предсуществующих пигментных невусов можно схематически представить в следующем виде: повреждение - невусные клетки - воспаление и пролиферация поврежденной ткани - длительная пролиферация + воздействие эндогенных канцерогенных факторов (иммунологических, эндокринных, нейрогенных и др.) - нарушение структуры ДНК клетки - нарушение дифференцировки клетки - изменение белковой структуры клетки с возникновением новых мембранных антигенов - гипореактивность - бесконечно долгое размножение (опухолевый рост).</p>\r\n<p>Что касается действия эндогенных канцерогенных факторов меланомы кожи, то, очевидно, что точкой их приложения являются длительно пролиферирующие нормальные клетки и ткани, которые под воздействием этих факторов могут трансформироваться в опухолевые.</p>",
"diagnostics": "<p>Дерматоскопия -макроскопический осмотр образования при помощи дерматоскопа.</p>\r\n<p>Биопсия с последующим гистологическим анализом. Гистологическая диагностика представляет собой осмотр микропрепарата (тончайший срез исследуемого образца), подвергшегося специфической или неспецифической окраске. Помимо окраски с целью определения клеточного или тканевого атипизма, применяются также иммуногистохимический и иммуноферментный анализы</p>",
"treatment": "<p>Основным методом терапии является локальное иссечение первичной опухоли до фасции. Количество иссекаемых тканей зависит от распространенности опухолей и рассматриваются индивидуально, обычно с небольшим захватом здоровых тканей. Лекарственная терапия меланомы in situ проводится редко, только при гистологической верификации метастазирования опухоли. Поскольку к химиотерапии рак кожи в последние годы всё более устойчив, а химиопрепараты крайне токсичны, активно развивается иммунотерапия. Для лечения прогрессирующей меланомы используют препараты на основе альфа-интерферонов, интерлейкина и моноклональных антител.</p>\r\n<p>Третий вид терапии злокачественных опухолей – лучевая. Облучение назначается до операции с целью уменьшения объема хирургического вмешательства либо после операции.</p>\r\n<p>Комбинацию и методы врач подбирает индивидуально исходя из существующих особенностей меланомы in situ в каждом конкретном случае.</p>",
"prevention": "<p>Чтобы предотвратить переход доброкачественного процесса в злокачественное, люди входящие в группу риска должны регулярно наблюдаться у врача. Любыми видоизменения родинок, усиление пигментации, увеличение родимых пятен в размерах, уплотнение невусов должны стать поводом немедленного обращения к врачу. Люди, на теле которых множество родинок и невусов должны внимательно относиться к своему здоровью. Необходимо избегать попадания прямых солнечных лучей на места скопления родимых пятен, не допускать повреждения образований и регулярно посещать косметолога в целях профилактики. </p>\r\n<p> </p>",
"clinical_picture": "<p>Меланома in situ характеризуется появлением следующих клинических симптомов:</p>\r\n<ul>\r\n<li>Усилением пигментации пятна, его ростом и выраженным затвердением. В отличие от доброкачественных родинок, форма in situ не имеет осевой симметрии, ее очертания неровные. Пигментированное пятно состоит из мелких скоплений. Если у доброкачественных родинок цвет всегда равномерный, то у радиальной меланомы он может сочетаться светло-коричневым и песочным оттенками.</li>\r\n<li>Появление красного ободка вокруг меланомы и застойных явлений</li>\r\n<li>Появление пигментных разрастаний в виде лучей, отходящих от меланомы в разные стороны.</li>\r\n</ul>\r\n<p>В некоторых случаях первым клиническим симптомом прогрессирующей меланомы in situ является увеличение крупных лимфатических узлов, тогда как давно существующая родинка или невус на поверхности кожи не изменяется по своей окраске и в размерах. Прогрессирующее увеличение родинки или невуса на поверхности кожи, а также его затвердение и изменение окраски является первым симптомом того, что заболевание перешло в злокачественную форму течения.</p>\r\n<p>Очень часто рядом с растущим пигментным пятном начинают появляться различные плотные узелки усиленной пигментации. </p>\r\n<p> </p>",
"image": null,
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"standard_type": 3,
"danger": 1,
"published": 2,
"parent": null,
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{
"id": 9159,
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"code": "D03.6",
"name": "Меланома in situ верхней конечности, включая область",
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"slug": "d03.6_melanoma_in_situ_verhney_konechnosti_vklyuchaya_oblast",
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"image": null,
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"standard_type": 3,
"danger": 1,
"published": 1,
"parent": 7997,
"block_rubric": 36,
"standards": []
}
]
}