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},
"code": "B83.4",
"name": "Внутренний гирудиноз",
"icd_name": "Внутренний гирудиноз",
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"age_min": 1,
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],
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"slug": "b83.4_vnutrenniy_girudinoz",
"lead": "заражение кровососущими пиявками внутренних полостей тела, открытых для проникновения паразитов",
"description": "",
"etiology": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Возбудители патологии – различные виды пиявок. Практически повсеместно распространены пиявки рода Haemopis, Limnatis, Hirudo (медицинские), вида Tyrannobdella rex (королевская). Обитают паразиты во влажной траве, торфяных болотах, стоячих пресных водоемах. Являются гермафродитами и активными хищниками, питаются кровью зверей, птиц, человека, присасываясь с помощью хоботков или хитиновых челюстей. Нападают преимущественно в ночное время.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Факторы риска</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Основные факторы риска гирудиноза связаны с профессиональной деятельностью, туризмом, проживанием в эндемичных регионах. Так, наиболее часто заражаются:</span></p>\r\n<ul style=\"margin-top: 0; margin-bottom: 0; padding-inline-start: 48px;\">\r\n<li><span style=\"font-size: 7pt; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">путешественники, проходящие маршруты по джунглям, заболоченной местности;</span></li>\r\n<li><span style=\"font-size: 7pt; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">жители регионов с высокой влажностью, большим числом непроточных озер;</span></li>\r\n<li><span style=\"font-size: 7pt; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">работники водоканалов;</span></li>\r\n<li><span style=\"font-size: 7pt; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">ветеринары;</span></li>\r\n<li><span style=\"font-size: 7pt; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">профессиональные рыболовы и охотники.</span></li>\r\n</ul>",
"pathogenesis": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Выделяя гирудин, являющийся сильным антикоагулянтом, а также гистаминоподобное вещество, расширяющее капилляры, пиявки вызывают кровотечение в месте присасывания. Возможны развитие анемии, головные боли и другие симптомы в зависимости от локализации паразита. Наиболее опасно присасывание пиявки к голосовым складкам или к стенке трахеи, т.к. это может привести к асфиксии.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Другой фактор патогенеза - механические повреждения, связанные с движением пиявки и травмированием ею нежных тканей. Последний фактор обычно проявляет себя при внутреннем гирудинозе, когда пребывание червя в полостях тела, протоках и внутренних органах может вызвать закупорку ходов, раздражение, спазматические явления и т. д.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Данные патологические процессы отягчают протекание гирудиноза. Наиболее тяжело гирудиноз протекает у лиц, предрасположенных или страдающих нарушениями механизма свертываемости крови.</span></p>",
"diagnostics": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Диагностика гирудиноза осуществляется врачами различных специальностей – это зависит от локализации возбудителя. Чаще всего больные попадают на прием к оториноларингологу, гинекологу и хирургу. Важен сбор анамнеза на предмет пребывания во влажных, заболоченных местностях, факты употребления воды из непроточных источников, колодцев. Дополнительно проводятся лабораторно-инструментальные и клинические исследования:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Физикальный осмотр. При наружном расположении возбудитель заметен и может быть удален. У пациента с внутренним гирудинозом объективный осмотр выявляет симптомы астении, бледность, сухость кожных покровов, нередко тахикардию, дисфонию, одышку. При пальпации живота отмечается урчание, вздутие, определяются диффузная или локальная болезненность, спленомегалия. Обязательна визуальная оценка рвоты, кала и мочи.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Эндоскопические исследования. Инструментальный осмотр полости носа (риноскопия), ротоглотки, органов дыхания (ларингоскопия, трахеобронхоскопия), а также различных отделов пищеварительного тракта (эзофагогастроскопия, колоноскопия) проводится по показаниям при подозрении на органный гирудиноз. Если в ходе исследования обнаруживается пиявка, производится ее удаление, прижигание места присасывания.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Лабораторные исследования. В общем анализе крови – нормохромная или гипохромная анемия, незначительный лейкоцитоз, редко эозинофилия, ускорение СОЭ. Может выявляться повышение активности СРБ, трансаминаз, нарушения свертывания крови, снижение ферритина. Общеклинический анализ мочи обнаруживает лейкоцитурию, эритроцитурию, гематурию.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Инструментальные методы. Для исключения новообразований проводится рентгенография (либо низкодозовая МСКТ) легких, МРТ гортани, глотки, пищеварительного тракта, ирригоскопия. Рекомендуется УЗИ органов брюшной полости, малого таза. В некоторых случаях выполняется диагностическая лапароскопия.</span></li>\r\n</ul>\r\n<p> </p>\r\n<p><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\"> </span></p>",
"treatment": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Лечение висцерального гирудиноза, как правило, включает удаление пиявки при эндоскопическом исследовании. В стационарных условиях манипуляция проводится только при наличии отягощенного по нарушениям свертывания анамнеза. Во время эндоскопии пиявку обрабатывают тампоном, смоченным спиртово-йодным раствором, заставляя прекратить присасывание, и удаляют. Ранку ушивают или коагулируют.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Медикаментозная терапия</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Больные с признаками осложнений должны быть госпитализированы. Пациенты с дыхательной недостаточностью, выраженной кровопотерей помещаются в палаты интенсивной терапии. После удаления возбудителя рекомендуется обогащение рациона белковой и железосодержащей пищей.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Важным этапом является восстановление кровопотери, коррекция железодефицитной анемии и ее последствий. Восстановление объема циркулирующей крови показано только в случае массивного кровотечения, проводится глюкозо-солевыми растворами, свежезамороженной плазмой, реже − эритроцитарной массой.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Местно применяются кровоостанавливающие повязки, химическое, лазерное коагулирование раны. Антибактериальные средства при гирудинозе назначаются по показаниям. Фармакологического антидота к компонентам железистого секрета пиявок не существует.</span></p>",
"prevention": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Специфической профилактики нет. Неспецифические меры – отказ от питья сырой воды из колодцев, озер, купания на необорудованных пляжах, в стоячих водоемах. Купальные костюмы должны быть закрытыми, необходимо надевать шапочку и очки, нельзя глотать воду.</span></p>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">В походах, особенно утренних, рекомендуется носить брюки, заправленные в обувь, носки, высокие резиновые сапоги, не расстегивать ворот рубашки. Можно использовать солевые повязки, химические вещества для отпугивания пиявок (инданол, диметилфолат), либо нанести на одежду, тело и обувь парфюм или жидкое мыло с резким запахом. Запрещается ходить босиком и в открытой обуви по влажной траве.</span></p>",
"clinical_picture": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">При носовом гирудинозе первые симптомы – назальные кровотечения, ощущение инородного тела, зуд, иногда нарушения обоняния и чувство заложенности. Поражение ротоглотки и гортани проявляется изменениями голоса, осиплостью, лающим приступообразным кашлем, а также сухостью, чувством «комка в горле», першением.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Нахождение пиявки внутри трахеи, нижних дыхательных путей вызывает нарастающие симптомы нехватки воздуха, одышку. При тяжелом течении пациенты принимают вынужденную позу для облегчения вдоха и выдоха, отмечают эпизоды кровохарканья и горлового кровотечения.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">При локализации пиявок в пищеводе возникают боли за грудиной, затруднения проглатывания пищи, тошнота, рвота с кровью. Гирудиноз ЖКТ практически сразу проявляется рвотой типа «кофейной гущи», дегтеобразным стулом либо наличием прожилок крови в испражнениях. Поражение мочеполовой системы (уретры, влагалища, мочевого пузыря) манифестирует с появления кровянистых выделений из половых путей, болезненных ощущений в промежности и над лобком, мочи красного цвета.</span></p>",
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"lead": "порок развития, характеризующийся двумя признаками: отсутствием связи пораженного участка с бронхиальной системой легкого и кровоснабжения из аномальных артерий, отходящих непосредственно от аорты или ее ветвей",
"description": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Секвестрацией легкого обозначают порок развития, при ко­тором часть легочной ткани, обычно аномально развитой и представляющей собой кисту или группу кист, оказывается от­деленной (секвестрированной) от нормальных анатомо-физио-логических связей (бронхов и сосудов малого круга кровооб­ращения) и снабжается кровью артериями большого круга, отходящими от аорты.</span></p>",
"etiology": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Секвестрация легкого является сложным пороком, вызванным комбинированным нарушением формирования различных бронхолегочных структур. Аномалия развивается в результате тератогенных влияний в раннюю внутриутробную фазу. Источником развития легочного секвестра являются добавочные выпячивания первичной кишки, рудименты дивертикула пищевода, отделившиеся от организующихся легких и затем теряющие связь с первичной кишкой и бронхиальным деревом. Иногда может оставаться связь рудимента легкого с пищеводом или желудком с помощью соустья-тяжа (бронхолегочно-кишечная мальформация).</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Согласно теории тракции, развитию секвестрации легкого способствует нарушение редукции ветвей первичной аорты с трансформацией их в аномальные сосуды. Через эти сосудистые ветви зачаточные фрагменты легкого отграничиваются от нормальной легочной закладки.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Секвестрация легкого часто комбинируется с другими пороками развития: </span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">ЭЛС - с неиммунной водянкой плода, анасаркой, гидротораксом новорожденного; </span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">ИЛС – с врожденной аденоматоидной мальформацией легкого 2-го типа, рабдомиоматозной дисплазией, трахео- и бронхопищеводными свищами, воронкообразной деформацией грудной клетки, открытым средостением, диафрагмальной грыжей, гипоплазией почки, дефектами позвоночника и тазобедренных суставов.</span></li>\r\n</ul>",
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"diagnostics": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Диагноз устанавливают по совокупности данных обзорной рентгенографии и КТ легких, бронхографии, бронхоскопии, УЗИ брюшной полости, аортографии, ангиопульмонографии.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Рентгенологически интралобарная секвестрация легких (в отсутствии связи с бронхом и воспаления) определяется как затенение неправильной формы разной степени интенсивности с просветлением в толще или как полостное образование с горизонтальным уровнем жидкости или без него. При обострении вокруг секвестра в нижней доле легкого отмечается выраженная деформация сосудисто-бронхиального рисунка, умеренная перифокальная инфильтрация легочной ткани. При бронхографии наблюдается деформация и смещение бронхов, соседних с пораженным сегментом легкого. Бронхоскопическая картина секвестрации легкого, сообщающейся с дыхательными путями, соответствует катарально-гнойному эндобронхиту на стороне пораженного легкого.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Брюшнополостная ЭЛС выявляется на УЗИ как четко отграниченное образование однородной эхогенности с кровоснабжением через ветви крупных артерий. Диагноз окончательно подтверждается МСКТ легких и ангиопульмонографией с установлением наличия, количества и топографии аномальных сосудов, питающих область секвестрации. Радиоизотопное сканирование печени и перитонеография помогают отграничить правостороннюю секвестрацию легких от патологии органов ЖКТ. Секвестрация легкого нередко выявляется в ходе хирургического вмешательства по поводу хронического гнойного процесса в легком.</span></p>",
"treatment": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">При секвестрации легких требуется проведение оперативного вмешательства – удаление аномального участка легочной ткани. При выявлении бессимптомной внутридолевой секвестрации легких возможно выполнение сегментэктомии, однако чаще всего требуется удаление всей пораженной легочной доли (обычно нижней) – лобэктомия. </span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Тактика хирургического лечения внедолевой формы заключается в удалении секвестрированного участка (секвестрэктомии). Наличие при секвестрации легких аномальных крупных артериальных сосудов нетипичной локализации делает важным тщательную предварительную диагностику во избежание их интраоперационного повреждения и развития тяжелого угрожающего жизни кровотечения.</span></p>",
"prevention": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Специфические методы профилактики не разработаны. В период гестации необходимо отказаться от курения, алкогольных напитков и наркотических веществ. Запрещено принимать фармацевтические препараты без назначения врача. Важно избегать контактов с инфекционными больными, особенно на первых неделях беременности.</span></p>",
"clinical_picture": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Выраженность симптоматики зависит от места расположения секвестра, наличия или отсутствия сообщения с дыхательными путями, распространенности воспалительного процесса и степени гипоплазии легочных тканей. </span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Интралобарная секвестрация чаще проявляется на фоне инфицирования, воспалительного процесса, нагноения, прорыва кисты. </span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Нагноение кистозного образования выражается лихорадкой, слабостью, повышенным потоотделением, умеренным болевым синдромом, одышкой во время физических нагрузок, а прорыв абсцесса – гнойной мокротой. </span><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Редко патология сопровождается кровохарканьем, легочными кровотечениями и плевральными осложнениями. </span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Обычно заболевание обретает хроническое течение, однако наблюдаются вялые обострения и ремиссии. </span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Для экстралобарной формы характерна поздняя манифестация после пубертатного периода. При внедолевых секвестрах может сдавливаться пищевод, желудок и другие органы. В таком случае наблюдаются одышка, синюшный окрас кожных покровов и нарушения прохождения пищи по пищеводу. Возможные такие осложнения как: пневмомикоз, туберкулез, профузное легочное кровотечение, массивный гемоторакс, злокачественный опухолевый процесс, острая сердечная недостаточность.</span></p>",
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}
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}