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},
"code": "A82",
"name": "Бешенство",
"icd_name": "Бешенство",
"gender": 1,
"age_min": 0,
"age_max": 100,
"cause": [
2,
5,
9
],
"periodicity": 1,
"slug": "a82_beshenstvo",
"lead": "Острое природно-очаговое вирусное заболевание, распространенное преимущественно среди млекопитающих и передающееся через слюну",
"description": "",
"etiology": "<p>Бешенство – это вирусная инфекция, вызываемая Neuroiyctes rabid из семейства Рабдовирусов. </p>\r\n<p>В природе вирус циркулирует среди теплокровных животных и птиц. Источником инфекции является любое больное бешенством животное. Наиболее часто человек заражается от собак, кошек, волков, лисиц, летучих мышей, ворон, крупного рогатого скота. Обычно такие животные и птицы ведут себя неадекватно, нападают на людей и других зверей, кусая их и заражая таким образом. Считается, что больной бешенством человек, если укусит другого, также может быть источником инфекции. Вирус передается со слюной: при укусе и даже просто попадании слюны на кожу и слизистые (в связи с возможным наличием в этих местах микроповреждений, не заметных для глаза).</p>",
"pathogenesis": "<p>Инкубационный период (время от момента попадания возбудителя в организм до появления первых симптомов) длится в среднем от 10 дней до 3-4 месяцев. Зарегистрированы единичные случаи заболевания с инкубационным периодом около года. Сроки появления первых симптомов зависят от многих факторов: места укуса (самые опасные – в голову, половые органы, кисти рук), от количества вируса, попавшего в организм, состояния иммунной системы. Даже вид животного в этом случае играет роль. Следует знать, что любой укус животного рассматривается как потенциальный риск бешенства, и необходимо немедленно обращаться за медицинской помощью.</p>",
"diagnostics": "<p>Диагностика основывается на данных анамнеза: укус животного или ослюнение кожи. Затем играют роль специфические признаки бешенства: водобоязнь, к раздражителям (звукам, свету, сквозняку), обильное , приступы психомоторного возбуждения с судорогами (даже в ответ на малейшее движение воздуха).</p>\r\n<p>Из лабораторных методов можно отметить обнаружение антигенов вируса бешенства в отпечатках с поверхности роговицы. В анализе крови отмечается лейкоцитоз за счет увеличения содержания лимфоцитов. После гибели больного на вскрытии в веществе головного мозга обнаруживают тельца Бабеша-Негри.</p>",
"treatment": "<p>Статистически достоверных методов лечения бешенства не существует. Если у больного уже появились начальные признаки, то заболевание неизлечимо. Помочь больному можно только в инкубационный период, причем чем раньше, тем лучше. Для этого вводят вакцину против бешенства, но эта мера считается профилактической.</p>\r\n<p>Когда у больного уже появились признаки бешенства, обычно проводят так называемое симптоматическое лечение, чтобы облегчить его состояние. Для этого человека помещают в отдельную палату, изолируют его от света, шума, сквозняка (чтобы не провоцировать судороги). Из медикаментов применяют наркотические вещества, противосудорожные препараты, мышечные релаксанты. При наличии грубых дыхательных расстройств больного подключают к аппарату искусственной вентиляции легких. Эти манипуляции продлевают жизнь больному на несколько часов или даже дней, но исход все равно неблагоприятный: человек умирает. Введение антирабического иммуноглобулина и вакцины, когда уже появились симптомы бешенства, не эффективно!</p>\r\n<full></full>\r\n<p>С 2005 г. во всем мире зарегистрировано несколько случаев выздоровления от бешенства без применения антирабической вакцины. В 2005 г. в США 15-летняя девушка выжила в результате введения ее в искусственную кому с момента появления признаков бешенства. Пока она находилась в коме, ей применяли препараты, стимулирующие иммунную систему. Такое лечение было основано на предположении, что человеческий организм просто не успевает выработать антитела против вируса бешенства, и если «выключить» нервную систему на какое-то время, то есть надежда на исцеление. Произошло чудо – и девушка выздоровела. Подобный метод лечения назвали «протокол Милуоки». Позже этот протокол пробовали применить к другим случаям заболевания бешенством: из 24 попыток успехом завершилась только одна, остальные 23 человека погибли.</p>\r\n<p>В 2008 г. удалось спасти 15-летнего мальчика из Бразилии. Для его лечения применяли протокол Милуоки, противовирусные средства, успокоительные и средства для анестезии. В 2011 г. выжил 8-летний ребенок, в 2012 г. – еще 5 человек. Во всех случаях лечение проводилось согласно протокола. Ученые до сих пор не сошлись во мнении, что же именно помогло этим больным избежать смерти. Предполагается, что главную роль сыграл необычайно сильный иммунитет и, возможно, ослабленная форма вируса, вызвавшего заболевание.</p>\r\n<p>В 2009 г. в США был зарегистрирован случай выздоровления у асоциальной женщины с симптомами бешенства, предположительно возникшими после укуса летучей мыши. Этот эпизод подтолкнул ученых к мысли, что у человека могут возникать абортивные формы бешенства по аналогии с животными. Ведь известно, что от 1% до 8% животных, которые были укушены заведомо больным животным, не заболевают бешенством.</p>",
"prevention": "<p>Существуют две российские вакцины от бешенства — «культуральная антирабическая вакцина» (КАВ) (концентрация 0,5 МЕ/мл) и \" концентрированная культуральная антирабическая вакцина\" (КоКАВ) (концентрация 2,5 МЕ/мл) . У вакцины КАВ есть и другое название — Рабивак-Внуково-32 или просто Рабивак. КАВ вводится в больших объемах и большее число раз, так что если есть возможность выбора, выбирайте КоКАВ.</p>\r\n<p>На Российском рынке еще представлена французская вакцина Верораб (фирмы Aventis Pasteur), содержащая инактивированный вирус (штамм Wistar, Rabies PM/Wi38–1503–3M) — 2,5 МЕ и немецкая Рабипур (фирмы Ciron Behring), состоящая из инактивированного (убитого) вируса бешенства (штамм Flury LEP).</p>\r\n<p>Есть еще французская прививка, которая называется Имогам Раж. Это иммуноглобулин, который вводится однократно, одновременно с вакциной и показан лицам с подозрением на инфицирование вирусом бешенства, особенно в случае значительных повреждений (в соответствии с рекомендациями ВОЗ — одиночные или множественные укусы или царапины с нарушением целостности кожных покровов).</p>\r\n<p>Побочные эффекты у всех вакцин примерно одинаковы и включают в себя местные реакции в виде болезненности, отека и уплотнения, , общее , , \"></a>, и аппетита, , а также иногда случается аллергия на компоненты вакцины.</p>",
"clinical_picture": "<p>1. Продромальная фаза (предвестники). У 50-80% больных первые признаки бешенства всегда связаны с местом укуса: появляется боль и , рубец вновь припухает и краснеет. Другие симптомы: тела, общее , \">, \">, затруднённое глотание, . Возможны повышение зрительной и слуховой чувствительности, беспричинный \">, нарушения сна (, кошмары).</p>\r\n<p>2. Энцефалитная фаза (возбуждение). Спустя 2-3 дня развивается период возбуждения, для которого характерны периодические приступы болезненных спазмов (судорог) всех мышц, возникающих от малейшего раздражителя: яркий свет (), шум (акустофобия), дуновение воздуха (аэрофобия). Иногда в этой стадии на фоне приступов больные становятся агрессивными, кричат, мечутся, рвут одежду, ломают мебель, обнаруживая нечеловеческую «бешенную» силу. Между приступами часто наступает , слуховые и .</p>\r\n<p>Температура тела повышается до 40-41 градуса, резко выражены , постуральное снижение АД, повышенное слёзотечение, \"> и саливация (обильное отделение слюны). Затруднения глотания слюны и вспенивание её воздухом при глотании дают характерный симптом бешенства — «пена изо рта».</p>\r\n<full></full>\r\n<p>Вслед за острым энцефалитом развивается стволовая симптоматика. Исчезает корнеальный рефлекс, пропадает глоточный рефлекс. Развивается гидрофобия — судорожные сокращения глотательной мускулатуры при виде воды или звуках льющейся воды.</p>\r\n<p>Появление уже на ранней стадии болезни симптомов дисфункции ствола головного мозга является отличительным признаком бешенства от других энцефалитов.</p>\r\n<p>3. Заключительная фаза (параличи). Если больной не скончался от длительного спазма дыхательных мышц, то ещё через 2-3 дня болезнь переходит в последнюю стадию, для которой характерно развитие параличей конечностей и нарастание стволовой симптоматики в виде поражения черепно-мозговых нервов (, лицевого нерва, неврит зрительного нерва), нарушение функции тазовых органов (приапизм, спонтанная эякуляция). Психомоторное возбуждение и судороги ослабевают, больной может пить и есть, дыхание становится более спокойным («зловещее успокоение»). Через 12-20 часов наступает смерть от паралича дыхательного центра или остановки сердца, как правило, внезапно, без агонии.</p>\r\n<p>Общая длительность болезни не превышает 5-7 дней.</p>",
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{
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"code": "A83",
"name": "Комариный вирусный энцефалит",
"icd_name": "Комариный вирусный энцефалит",
"gender": 0,
"age_min": 10,
"age_max": 89,
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"slug": "a83_komarinyy_virusnyy_encefalit",
"lead": "Нарушение здоровья, относящееся к группе вирусные инфекции центральной нервной системы",
"description": "Комариный энцефалит - острая сезонная нейро-инфекция с общеинфекционными проявлениями и тяжёлым поражением вещества мозга. ",
"etiology": "<p>Вирус японского энцефалита относится к семейству Flaviviridae, входит в экологическую группу арбовирусов. Вирус содержит РНК, его размеры не превышают 15—22 нм. При кипячении сохраняется в течение двух часов. Спирт, эфир и ацетон оказывают угнетающее действие на активность возбудителя только через 3 дня. При низких температурах может сохраняться более года. </p>\r\n<p>Источник заражения - дикие животные, птицы. </p>\r\n<p>Переносчиками вируса являются комары (Culex pipiens, Culex trithaeniorhynchus, Aedes togoi, Aedes japonicus).Заражение человека происходит в результате попадания слюны комара в ранку, возникающую при укусе. </p>",
"pathogenesis": "<p>После укуса инфицированным комаром вирус гематогенным путём попадает в ЦНС и в связи с выраженной нейротропностью быстро размножается в нервных клетках. По достижении максимальной концентрации вирус повторно выходит в кровь и действует общетоксически, что соответствует окончанию инкубационного периода и началу клинических проявлений. </p>\r\n<p>Наибольшие морфологические изменения обнаруживают в ЦНС. Макроскопически мозговые оболочки отёчны, гиперемированы, с точечными кровоизлияниями. Вещество мозга набухшее, дряблое, с локальными кровоизлияниями и очагами размягчения. Выраженные изменения отмечают в области зрительных бугров и стриарных образований. </p>",
"diagnostics": "<p>Специфическая лабораторная диагностика включает в себя: </p>\r\n<ul>\r\n<li>выделение вируса методом ПЦР (он может быть обнаружен особенно в первые 7 дней болезни в крови, моче и цереброспинальной жидкости), </li>\r\n<li>обнаружение вирусного антигена с помощью реакции иммунофлюоресценции и иммуноферментного метода; </li>\r\n<li>выявление 4-кратного и более нарастания титра антител в парных сыворотках, взятых в первые дни болезни и через 2-3 нед, с помощью РСК, РТГА, РН и др. </li>\r\n<li>Иногда применяют кожно-аллергическую пробу с введением суспензии мозга зараженных мышей. </li>\r\n</ul>\r\n<p>К инструментальным методам диагностики относятся: </p>\r\n<ul>\r\n<li>Эхо-энцефалография; </li>\r\n<li>ЭЭГ; </li>\r\n<li>Офтальмоскопия; </li>\r\n<li>КТ и МРТ головного мозга. </li>\r\n</ul>",
"treatment": "<p>Этиотропная составляющая предполагает назначение противовирусного фармпрепарата рибавирина. Параллельно осуществляется терапия интерфероном и его аналогами. Возможно использование специфического иммуноглобулина. </p>\r\n<p>Патогенетическая составляющая заключается в коррекции жизненно важных функций, применении противоотечных средств, антигипоксантов, нейропротекторов. Зачастую возникает необходимость в назначении глюкокортикоидов, обладающих выраженным противовоспалительным и противоотечным действием. </p>\r\n<p>Симптоматическая терапия подразумевает использование по мере необходимости психотропных средств (нейролептиков, транквилизаторов), противорвотных препаратов. </p>\r\n<p>Восстановительное лечение предусматривает сосудистую и нейропротекторную терапию с целью скорейшего и как можно более полного восстановления церебральных структур и их функций. При наличии парезов обязательными компонентами реабилитации являются массаж и ЛФК; возможно использование физиотерапии — электрофореза, электромиостимуляции, рефлексотерапии. </p>\r\n<p>При нарушениях психики необходима консультация психиатра с осуществлением коррекционной терапии, психотерапии, социальной адаптации.</p>",
"prevention": "<p>В очагах японского энцефалита проводят комплекс противокомариных мероприятий, осуществляют меры по защите от нападения комаров и созданию активного иммунитета у населения. Иммунизацию проводят по эпидемическим показаниям населению эндемических очагов с помощью формолвакцины. Для экстренной пассивной профилактики применяют однократно 10 мл гипериммунной лошадиной сыворотки или 6 мл иммуноглобулина. </p>",
"clinical_picture": "<p>Инкубационный период (от заражения до появления симптомов) 5-14 дней. Начало острое, температура до 40 °С в течение 7-10 дней. Первые дни - озноб, головная боль, ломота, тошнота, рвота, мышечная гипертония. </p>\r\n<p>С 3-4-го дня болезни в случаях с тяжелым течением на первый план выходят признаки поражения центральной нервной системы. Нарастает головная боль, отмечаются заторможенность или периодически психомоторное возбуждение, бред и галлюцинации, нередки клонические или тонические судороги. </p>\r\n<p>В течение 2-3 дней часто развивается коматозное состояние. Помимо общемозговых симптомов, наблюдаются менингеальный синдром и разнообразные очаговые неврологические симптомы (спастические парезы и параличи, нарушение речи, гипертонус мышц, гиперкинезы (патологические непроизвольные движения), эпилептиформные припадки, признаки поражения ядер черепных нервов и др). </p>\r\n<p>Развиваются резкая одышка, потливость, покраснение лица, шеи и верхней части туловища, пульс до 120-140 и более в минуту, понижение или, реже, повышение артериального давления. Может быть небольшое увеличение печени и селезенки. </p>\r\n<p>Реконвалесценция (выздоровление) длительная. В периоде реконвалесценции продолжительностью 4-7 недель температура тела нормальная, сохраняются некоторые остаточные симптомы органического поражения головного, мозга (парезы, мышечная слабость). </p>",
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