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},
"code": "A22",
"name": "Сибирская язва",
"icd_name": "Сибирская язва",
"gender": 2,
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"age_max": 100,
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4,
5,
7
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"slug": "a22_sibirskaya_yazva",
"lead": "Острая сапрозоонозная инфекционная болезнь с преимущественно контактным механизмом передачи возбудителя. ",
"description": "Чаще всего протекает в доброкачественной кожной форме, реже — в генерализованной. Относят к опасным инфекциям. Возбудитель сибирской язвы рассматривают в качестве биологического оружия массового поражения (биотерроризм).",
"etiology": "<p>Возбудитель — крупная грамположительная неподвижная палочка Bacillus anthracis рода Bacillus семейства Bacillaceae.</p>\r\n<p>Резервуар инфекции — почва, в которой вследствие повторения биологических циклов (спора–вегетативная клетка) возбудитель длительно сохраняется и накапливается. Такая особенность B. anthracis способствует созданию долговременно активных почвенных очагов («проклятые» поля) и потенциально опасных территорий. Это приводит к периодическим эпизоотиям и случаям сибирской язвы у людей. Болезнь развивается при попадании в организм вегетативных клеток или спор возбудителя. Источники B. anthracis для человека — крупный (буйволы, коровы) и мелкий (козы, овцы) рогатый скот, лошади, верблюды, а также (в редких случаях) дикие животные (зайцы, волки, медведи, песцы и др.).</p>\r\n<full></full>\r\n<p>Больные животные выделяют возбудитель с мочой, калом и другими выделениями. Заболеваемость людей зависит от степени распространения этой инфекции среди животных. Механизмы передачи возбудителя к человеку — контактный (при нарушении правил личной гигиены при уходе за больными животными, забое и разделке туш, снятии шкур, контакте с шерстью, шкурой и другими продуктами животноводства, контаминированными B. anthracis), аспирационный (воздушно-пылевым путём при вдыхании инфицированной пыли, костной муки), фекально-оральный (пищевой путь при употреблении мяса заражённого животного) и трансмиссивный (через укусы слепней, мух-жигалок, комаров). Факторы передачи — почва, вода, воздух, пища, предметы быта, животные и продукты их жизнедеятельности, эктопаразиты.</p>",
"pathogenesis": "<p>Заражение происходит при попадании как вегетативной формы, так и спор возбудителя в организм человека, где они благодаря капсуле защищены от фагоцитоза и продуцируют экзотоксин, вызывающий повреждение эндотелия сосудов. Микроциркуляторные нарушения и повышение проницаемости сосудов — важное звено патогенеза сибирской язвы. В результате этих изменений в местах размножения возбудителя (кожа, лимфатические узлы, лёгкие, кишечная стенка) развиваются серозно-геморрагическое , периваскулярные кровоизлияния, геморрагические инфильтраты, резкий . При заражении аэрозольным и алиментарным путями возбудитель легко преодолевает лимфатический барьер, распространяется гематогенно. Инфекция принимает генерализованный характер с массивным обсеменением органов (септицемия), сопровождаясь развитием инфекционно-токсического шока, тромбогеморрагического синдрома и полиорганной недостаточности. При перкутанном заражении генерализацию инфекции наблюдают редко. ограничивается кожей, носит локальный характер, однако токсины вызывают повышенную проницаемость сосудов с развитием обширного отёка и местной анестезией.</p>",
"diagnostics": "<p>Диагноз кожной формы болезни устанавливают на основании характерных местных изменений: наличия чёрного струпа с венчиком гиперемии («чёрный уголёк на красном фоне»), студенистого безболезненного отёка и регионарного лимфаденита, появления общих симптомов после формирования карбункула.</p>\r\n<p>Особое значение для диагностики имеют эпидемиологические данные (профессия, уход за скотом, забой, разделка туш, работа с кожами, шкурами и т.д., ношение изделий из кожи и меха нефабричной выделки, употребление мяса, не прошедшего ветеринарно-санитарного контроля, особенно при вынужденном забое больных животных). При генерализованной форме болезни установить диагноз без эпидемиологических и лабораторных данных сложно.</p>\r\n<p>Разработаны тест-системы для определения генетического материала возбудителя сибирской язвы методом ПЦР. Применяют кожно-аллергическую пробу с антраксином, которая с 3-го дня болезни становится положительной в 82% случаев. При исследовании животноводческого сырья (шкуры, шерсть) применяют реакцию термопреципитации по Асколи и другие методы.</p>",
"treatment": "<p>Лечение сибирской язвы включает этиотропную и патогенетическую терапию, проводимую в зависимости от формы болезни и имеющихся клинико-лабораторных синдромов.</p>\r\n<p>Одновременно с этиотропной терапией однократно вводят специфический противосибиреязвенный иммуноглобулин в дозе 20–100 мл внутримышечно (доза зависит от тяжести состояния). Местная терапия заключается только в обработке поражённых участков кожи растворами антисептиков. Повязки не накладывают.</p>",
"prevention": "<p>Профилактические мероприятия подразделяются на ветеринарные и медико-санитарные.</p>\r\n<p>Ветеринарная служба осуществляет выявление, своевременную диагностику, забой больных животных, эпизоотологическое обследование очага, обеззараживание трупов, уничтожение мяса, шкур, шерсти павших животных, текущую и заключительную дезинфекцию в очаге, разрабатывает мероприятия, направленные на оздоровление скотомогильников, пастбищ, неблагополучных по сибирской язве территорий, а также плановую иммунизацию живой сибиреязвенной вакциной сельскохозяйственных животных в неблагополучных пунктах. Комплекс медико-санитарных мероприятий включает:</p>\r\n<ul>\r\n<li>контроль за соблюдением общесанитарных норм при заготовке, хранении, транспортировке и переработке сырья животного происхождения;</li>\r\n<li>вакцинопрофилактику живой споровой сухой бескапсульной вакциной — двукратно планово (на неблагополучных по сибирской язве территориях) и внеплановую (по эпидемическим показаниям с последующей ревакцинацией ежегодно);</li>\r\n<li>своевременную диагностику, госпитализацию и лечение больных;</li>\r\n<li>эпидемиологические обследования очага, текущую и заключительную дезинфекцию (4% хлорамином); · запрещено проводить посмертное вскрытие больных из-за возможности заражения спорами.</li>\r\n</ul>\r\n<p>Лицам, соприкасающимся с больными людьми или животными, в целях профилактики вводят противосибиреязвенный иммуноглобулин и антибактериальные препараты в течение 5 дней (табл. 17-28, 17-29). Наблюдение за контактными ведётся в течение 14 дней.</p>",
"clinical_picture": "<p>Инкубационный период зависит от пути проникновения и инфицирующей дозы возбудителя. Выделяют кожную (наружную, локализованную) и генерализованную (внутреннюю, висцеральную, септическую) формы сибирской язвы.</p>\r\n<p>Генерализованные формы могут быть первичными (карбункул отсутствует) и вторичными (при наличии карбункула). Кожная форма подразделяется на карбункулёзный, эдематозный, буллёзный, рожистоподобный и глазной варианты, а генерализованная форма — на лёгочный, кишечный и септический варианты.</p>\r\n<p>Наиболее часто (95–98% всех случаев сибирской язвы) встречается кожная форма. Инкубационный период при кожной форме болезни составляет от 2 до 14 сут. При своевременной антибактериальной терапии заболевание протекает относительно доброкачественно и заканчивается выздоровлением. Чаще наблюдается карбункулёзный вариант.</p>\r\n<p>В месте внедрения возбудителя (обычно на руках или голове) появляется красноватое или синеватое пятнышко, похожее на укус насекомого. Через несколько часов оно трансформируется в папулу медно-красного цвета, затем (в течение суток) в пузырёк, заполненный серозно-геморрагическим содержимым. Больных беспокоят жжение и . При расчёсывании или спонтанно пузырёк вскрывается с образованием язвочки, покрытой тёмно-коричневым струпом, формируется сибиреязвенный карбункул. Он расположен на плотном инфильтрированном основании, окружён венчиком яркой гиперемии. Образующиеся вокруг дочерние пузырьки также вскрываются, поэтому размеры струпа увеличиваются до 0,5–3,0 см в диаметре и более. Вокруг карбункула развивается резкий распространённый мягких тканей, имеющий желеобразную консистенцию. Болевая чувствительность в области карбункула и отёка из-за воздействия токсина на нервные окончания резко снижена или полностью отсутствует. Кожа в зоне отёка бледная. Регионарные лимфатические узлы плотные, подвижные, умеренно увеличены, слегка чувствительны при пальпации. При локализации карбункула в области кисти или предплечья возможен лимфангит. После уменьшения отёка (8–10-й день болезни) возвышается над поверхностью кожи, под ним идут процессы рубцевания и эпителизации язвы. Через 10–30 дней отторгается, язва полностью рубцуется. Карбункулы могут быть единичными и множественными (до десяти и более).</p>\r\n<full></full>\r\n<p>При кожной форме болезни общее состояние больного в первый день болезни остаётся удовлетворительным, на 2–3-й день появляются с ознобом\">Озноб\"> с ознобом\"><a href=\"/symptom/oznob/\" title=\"Перейти на страницу симптома Озноб\">озноб</a>, , \">, температура тела поднимается до 38–40 °С, отмечают тахикардию, артериальную гипотензию. Температура тела остаётся повышенной в течение 3–7 дней, затем критически падает до нормы, общее состояние пациента быстро улучшается, уменьшается в области карбункула, а потом отторгается и наступает полное выздоровление.</p>\r\n<p>Значительно реже после кратковременного улучшения внезапно появляется с ознобом\">Озноб\"> с ознобом\"><a href=\"/symptom/oznob/\" title=\"Перейти на страницу симптома Озноб\">озноб</a>, резко ухудшается общее состояние и развивается генерализованная инфекция. В настоящее время при современной антибиотикотерапии заболевание протекает относительно доброкачественно и заканчивается выздоровлением. Летальность при кожной форме болезни не превышает 2–3% при лечении, без антибиотикотерапии достигает 20%.</p>\r\n<p>Первичная генерализованная форма сибирской язвы развивается при аэрогенном или алиментарном пути заражения и крайне редко — при внедрении возбудителя через кожу или слизистую оболочку (например, губ). При этом в месте внедрения возбудителя карбункул не формируется. Генерализованная форма характеризуется бурным началом, потрясающим ознобом, гипертермией, резко выраженными симптомами интоксикации, головной болью, рвотой, тахикардией, прогрессирующей гипотензией, глухостью тонов сердца. Часто увеличиваются печень и селезёнка, появляются геморрагическая на коже, , симптомы поражения центральной нервной системы. При лёгочном варианте в первый день болезни возможны \">, боли в мышцах, катаральные явления, поэтому часто диагностируют ОРЗ или грипп, но уже через несколько часов развивается интоксикационный синдром, температура достигает 39–41 °С и на первый план выступают такие симптомы, как <a href=\"/symptom/odyshka/\" title=\"Перейти на страницу симптома Одышка\">чувство удушья</a>, боли в грудной клетке при дыхании, , с пенистой кровянистой мокротой, которая быстро сворачивается в виде желе. Кожа становится бледной, возникают , глухость тонов сердца, быстро прогрессирует \"><a href=\"/symptom/golovokruzhenie/\" title=\"Перейти на страницу симптома Головокружение\">падение</a> АД. Стремительно нарастают симптомы дыхательной недостаточности. Смерть наступает на 2–3-й день болезни от инфекционно-токсического шока и дыхательной недостаточности.</p>\r\n<p>Летальность составляет 80–100%. Положительный прогноз возможен при начале комплексной терапии до развития картины шока.</p>\r\n<p>Для кишечного варианта болезни, помимо общих симптомов, с первого дня болезни характерны режущие боли, преимущественно в нижней части живота, \">Рвота\">\">рвота\">кровавая \">Рвота\">\"><a href=\"/symptom/rvota/\" title=\"Перейти на страницу симптома Рвота\">рвота</a>, частый жидкий стул с примесью крови, быстро развивающиеся кишечника и перитонит. Исход также неблагоприятный. При всех вариантах болезни возможны осложнения: инфекционно-токсический , , менингит, острая дыхательная недостаточность.</p>",
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"code": "A23",
"name": "Бруцеллез",
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"lead": "инфекционное заболевание, которое передается человеку от больного животного",
"description": "<p>Бруцеллез - это <span style=\"color: #202122; font-family: Verdana; font-size: 7pt; white-space: pre-wrap;\">зоонозная инфекция, передающаяся от больных животных человеку, характеризующаяся множественным поражением органов и систем организма человека.</span></p>",
"etiology": "<p>Возбудитель заболевания – бруцеллы. Источником бруцелл являются сельскохозяйственные животные – мелкий и крупный рогатый скот, свиньи. Человек инфицируется при уходе за ними или при употреблении инфицированных продуктов. Входными воротами для проникновения инфекции являются пищеварительный тракт, трещины, царапины и другие повреждения на коже или слизистой оболочке. Проникнув в организм, бруцеллы с лимфотоком проникают в регионарные лимфоузлы, где вызывают воспалительные изменения. В дальнейшем бруцеллы поступают из первичных очагов в кровь и разносятся по всему организму, обусловливая образование гранулем во внутренних органах, <a title=\"Перейти на страницу симптома воспаление\" href=\"/symptom/vospalenie/\">воспаление</a> мелких кровеносных сосудов, поражение синовиальных оболочек, слизистых сумок суставов, сухожильных соединений, фасций, периферических нервов.</p>",
"pathogenesis": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Входные ворота инфекции — слизистая оболочка желудочно-кишечного тракта и верхних дыхательных путей, механически повреждённая кожа, конъюнктива глаза. Инфицирующая доза — 10-100 бактерий.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">После попадания в организм патогенные бактерии движутся к регионарным лимфоузлам. Там они размножаются, а затем проникают в кровь, выделяя токсины и приводя к появлению первых признаков заболевания.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Дальнейшее развитие и размножение бруцелл происходит в лимфатических узлах, откуда они периодически проникают в кровоток, приводя при неоднократных атаках к распространению инфекции по всему организму. В ответ на инфицирование происходит выработка антител, стимуляция фагоцитоза (поглощение иммунными клетками крови), что ведёт к исчезновению возбудителя бруцеллёза из крови и изменению клинической картины болезни (сглаживанию симптомов). Однако часто бактерии сохраняются в некоторых органах и тканях, где они избегают пагубного воздействия иммунной системы хозяина. Это приводит к хронизации болезни.</span></p>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Также при длительном течении болезни повышается чувствительность к чужеродным агентам в первую очередь за счёт развития аллергической реакций к бруцеллёзному антигену. Это в корне меняет ход иммунного процесса — на этом фоне наступает повторная генерализация, при которой бруцеллы выходят из метастатических очагов, вновь попадают в кровь, приводя к развитию рецидива.</span></p>",
"diagnostics": "<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">клинический анализ крови: аномально высокий уровень нейтрофилов со сдвигом влево, повышение СОЭ, низкий уровень тромбоцитов и лимфоцитов, низкая концентрация гемоглобина;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">общий анализ мочи: уменьшение количества или отсутствие мочи, появление в ней белка, цилиндрических телец, лейкоцитов и эритроцитов;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">биохимический анализ крови;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">бактериальный посев биоматериала (крови, мочи, спинномозговой жидкости) на среды Терского или Фервольд — Вольфа с добавлением сыворотки кролика, барана (сыворотка улучшает рост бактерий бруцеллёза);</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">иммунологические серологические реакции (ИФА): необходимы двукратные тесты с интервалом в 2-4 недели для оценки нарастания титра антител в острый период;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">ПЦР-диагностика (полимеразная цепная реакция) — высокоточный метод, особенно в период острой инфекции и обострения;</span></li>\r\n<li><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">пассажи на животных — микробиологическая операция, осуществляемая с лабораторными животными при внедрении в их ткани бактерий</span></li>\r\n</ul>",
"treatment": "<p>Назначается антибактериальная терапия при остром бруцеллезе и обострении хронического бруцеллеза. Симптоматическое лечение включает прием обезболивающих, противовоспалительных средств. В стадии ремиссии и при стихании острого процесса показаны физиотерапевтические процедуры, бальнеологическое лечение.</p>",
"prevention": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">К мерам профилактики бруцеллёза относятся следующие мероприятия:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">употребление в пищу только кипяченого молока;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">строгий ветеринарный контроль животных;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">информирование населения о возможности заражения бруцеллёзом;</span></li>\r\n<li><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">проведение вакцинации среди группы риска (прививка действует на протяжении 2-х лет).</span></li>\r\n</ul>",
"clinical_picture": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Длительность инкубационного периода – от 1 до 8 недель, в среднем – 2-4 недели. Она зависит от формы заболевания, при острой форме инкубационный период короче, при латентном носительстве – может достигать 3 месяцев.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Для всех форм бруцеллеза в начальной стадии характерны следующие симптомы:</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">- Общая инфекционная интоксикация – слабость, недомогание, головная боль, бессонница.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">- Гипертермия или лихорадка – длительное повышение температуры тела до субфебрильных цифр (до 38 °C) или волнообразная лихорадка с резкими подъемами и падениями. Продолжительность лихорадки – до нескольких месяцев, она сопровождается ознобом и сильным потоотделением. </span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">- Артралгии и миалгии – суставные и мышечные боли, чаще поражающие нижние конечности. Эти боли – характерный симптом бруцеллеза.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">По мере развития заболевания у пациентов могут появляться гепатолиенальный синдром – увеличение размеров печени и селезенки, генерализованная микролимфаденопатия – увеличение лимфатических узлов в несмежных областях, различные поражения нервной системы – от нарушения чувствительности и потери сознания до паралича конечностей, психических расстройств. При разных формах бруцеллеза присоединяются различные симптомы.</span></p>\r\n<p><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\"> </span></p>",
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