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},
"code": "N82.0",
"name": "Пузырно-влагалищный свищ",
"icd_name": "Пузырно-влагалищный свищ",
"gender": 0,
"age_min": 25,
"age_max": 100,
"cause": [
"0"
],
"periodicity": 1,
"slug": "n82.0_puzyrno-vlagalischnyy_svisch",
"lead": "патология, характеризующаяся образованием аномального сообщения между влагалищем и мочевым пузырем",
"description": "",
"etiology": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Сообщение между мочевым пузырем и влагалищем возникает вследствие разрушения стенок органов при травмах и патологических процессах в полости малого таза. Специалисты в сфере гинекологии и урологии выделяют несколько групп травматических, воспалительных и деструктивных причин, приводящих к формированию мочепузырно-влагалищных свищей. Основными из них являются:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Гинекологические оперативные вмешательства. До 70% пузырно-вагинальных фистул становятся следствием гистерэктомии при доброкачественных фибромиомах матки. К их формированию также приводят непредумышленные повреждения при кесаревом сечении, хирургическом лечении эндометриоза, рака матки, других заболеваний тазовых органов.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Патологические роды. Длительное сдавливание мягких тканей родовых путей при затяжных родах, вторичной слабости родовых сил, прохождении крупного плода, узком тазе матери вызывает ишемический некроз с последующим образованием свищевого хода. Травматические повреждения возникают при неправильном наложении щипцов и разрывах тканей.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Случайные травмы. В небольшом количестве случаев пузырно-генитальные свищи формируются после травматических разрывов тканей из-за ДТП, несчастных случаев на производстве и быту, изнасилований. Возможна перфорация стенок влагалища, мочевого пузыря во время мастурбации с введением в вагину или уретральный канал острых предметов.</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Онкологические заболевания репродуктивных органов. Стенки вагины, мочевого пузыря могут разрушаться из-за прорастания опухолью при раке шейки матки, влагалища, других злокачественных новообразованиях. Одними из наиболее сложных для лечения считаются фистульные ходы, образовавшиеся после лучевой терапии онкологической патологии.</span></li>\r\n<li><span id=\"docs-internal-guid-07c1b21f-7fff-2001-b262-2caf1f916bdc\"><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">Воспалительные процессы. Во влагалище, мочевой пузырь могут прорываться абсцессы малого таза с образованием свищей. Свищевые ходы между этими органами появляются вследствие повреждения их стенок при некоторых инфекционных болезнях — венерической лимфогранулеме, шистоматозе, актиномикозе, туберкулезе мочевыделительных органов.</span></span></li>\r\n</ul>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>",
"pathogenesis": "<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Начальным этапом образования пузырно-вагинальных свищей становится перфорация тканей, которые разделяют влагалище и мочевой пузырь. Если такое повреждение не было вовремя замечено и ушито, существующая разница давлений между органами и постоянное подтекание мочи не позволяют отверстию зарубцеваться. В результате за 7-14 дней возникает фистульный ход, выстланный эпителиальной тканью. Ситуация усугубляется при наличии воспалительных или деструктивных процессов в области свищевого канала. В 65-66% случаев мочепузырно-влагалищные фистулы проявляются в первые 10 дней после травмы, а окончательно формируются за 3-5 месяцев.</span></p>",
"diagnostics": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Диагностику мочеполовой фистулы осуществляет акушер-гинеколог или уролог. Пациентке назначают ряд исследований, который включает:</span></p>\r\n<ul>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">общий анализ крови;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">общий анализ мочи;</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">цистоскопию (эндоскопический осмотр мочевого пузыря);</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">кольпоскопию (инструментальный гинекологический осмотр);</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">экскреторную (внутривенную) урографию (рентген мочевыделительной системы с контрастом);</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">ретроградную цистографию (рентген мочевого пузыря с контрастом);</span></li>\r\n<li><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">КТ и МРТ органов малого таза и др.</span></li>\r\n</ul>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Для дифференцирования диагноза и выявления сопутствующих патологий также могут назначаться дополнительные исследования (УЗИ органов малого таза и почек, вагинография (рентген влагалища) с контрастом и др.), консультации нефролога и онколога.</span></p>",
"treatment": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Медикаментозных методов терапии расстройства не предложено. Самопроизвольное заживление фистулы, соединяющей вагину с мочевым пузырем, наблюдается у 2-3% больных женщин при небольшом размере свищевого отверстия. Ускорению процессов регенерации в подобных случаях способствует отвод мочи с помощью постоянного уретрального катетера. У некоторых пациенток эффективной оказывается коагуляции краев свища электротоком или препаратами серебра со стороны влагалища или мочевого пузыря. В остальных случаях рекомендовано одно из хирургических вмешательств по восстановлению поврежденной стенки влагалища.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">П</span><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-style: normal; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">о мнению большинства урогинекологов, наиболее оправдана отсроченная фистулопластика, которая выполняется спустя 4-6 месяцев после образования свища. За это время максимально стихают воспалительные процессы, вызванные травмирующим воздействием, может быть проведена качественная предоперационная подготовка — удалены лигатурные камни, санированы мочевой пузырь и влагалище, восстановлено кровоснабжение тканей. При выборе конкретной техники учитывают размеры и место расположения свища, наличие рубцовых изменений, удаленность от устьев мочеточников, эластичность влагалищных стенок. Наиболее распространены:</span></p>\r\n<p> </p>\r\n<ul style=\"margin-top: 0; margin-bottom: 0; padding-inline-start: 48px;\">\r\n<li style=\"list-style-type: disc; font-size: 8pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Влагалищное иссечение свища. Операция отличается физиологичностью, малой травматичностью, сохранением целостности мочевого пузыря, более простым способом ушивания фистульного хода, сравнительно быстрым выздоровлением и отсутствием тяжелых осложнений. Метод показан для иссечения небольших неосложненных свищей при хорошей подвижности и растяжимости тканей влагалища. Ограничениями для проведения таких операций служат грубые рубцовые изменения вагины и глубокое залегание фистульного канала, при устранении которого может повредиться интравезикальный участок с устьями мочеточников.</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 8pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Трансабдоминальное иссечение свища. Закрытие дефекта через разрез передней брюшной стенки и мочевого пузыря показано при наличии больших по размеру фистул, вовлечении мочеточников, обнаружении комбинированных свищей, сопутствующей кишечной патологии. При более высокой травматичности преимуществами способа считаются хороший доступ и достаточный обзор для эффективного удаления измененных тканей, сохранение нормальной уродинамики после операции, возможность ликвидации даже сравнительно больших и сложных дефектов с качественным ушиванием вовлеченных органов.</span></p>\r\n</li>\r\n<li style=\"list-style-type: disc; font-size: 8pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre;\" dir=\"ltr\">\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Реконструктивная пластика. 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"prevention": "<p><span id=\"docs-internal-guid-48aeccb6-7fff-f246-0e45-787b44a4ec6a\"><span style=\"font-size: 7pt; font-family: Verdana; background-color: transparent; font-variant-numeric: normal; font-variant-east-asian: normal; vertical-align: baseline; white-space: pre-wrap;\">В целях профилактики расстройства рекомендованы регулярные осмотры у гинеколога для раннего выявления заболеваний, требующих хирургического лечения, своевременная постановка на учет для снижения риска осложнений в родах, бережное ведение родов, технически точное выполнение гинекологических, урологических операций.</span></span></p>",
"clinical_picture": "<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Заболевание характеризуется постоянным непроизвольным выделением мочи из влагалища. При этом самостоятельное мочеиспускание отсутствует полностью, а при небольшом размере свища сохраняется незначительно. Количество непроизвольно подтекаемой жидкости может быть различным: от нескольких капель с сохранением самостоятельного мочеиспускания до тотального выделения мочи только через влагалище. Характер мочеиспускания зависит, в первую очередь, от размера и локализации свища.</span></p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">Пациентки могут замечать непроизвольное выделение мочи сразу после операции или в течение ближайших месяцев. Иногда перед появлением подтекания мочи возникает боль внизу живота, гематурия, повышается температура тела, мочеиспускание становится частым и болезненным. После формирования свища эти симптомы проходят.</span></p>\r\n<p> </p>\r\n<p style=\"line-height: 1.38; margin-top: 0pt; margin-bottom: 0pt;\" dir=\"ltr\"><span style=\"font-size: 6.999999999999999pt; font-family: Verdana; color: #000000; background-color: transparent; font-weight: 400; font-style: normal; font-variant: normal; text-decoration: none; vertical-align: baseline; white-space: pre-wrap;\">При длительном истечении мочи кожа наружных половых органов и внутренней поверхности бёдер пропитывается жидкостью и набухает. Также пациентки отмечают неприятный запах и боли в области мочевого пузыря, а при появлении язв и очагов некроза — болезненность и невозможность половых контактов.</span></p>",
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